Magnetic resonance imaging detects changes in structure and perfusion, and response to therapy in early cystic fibrosis lung disease

MO Wielpütz, M Puderbach… - American journal of …, 2014 - atsjournals.org
… in early cystic fibrosis (CF) lung disease. Summary of (A) individual lobar and (B) whole-lung
in children with acute exacerbation of CF lung disease before and after antibiotic therapy. …

Computed tomography and magnetic resonance imaging in cystic fibrosis lung disease

M Eichinger, CP Heussel, HU Kauczor… - Journal of Magnetic …, 2010 - Wiley Online Library
… of lung morphology and is so far the most reliable imaging modality for monitoring cystic
fibrosis (CF) lung disease. … in the CF lung. It is thought to be less sensitive to detect small airway …

Risk factors for the progression of cystic fibrosis lung disease throughout childhood

DB Sanders, Z Li, A Laxova, MJ Rock… - Annals of the …, 2014 - atsjournals.org
lung disease and survival in cystic fibrosis (CF) for successive birth cohorts, the progression
of CF lung disease … important in the progression of CF lung disease and early mortality (2–10…

Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease

AS Verkman, Y Song… - American Journal of …, 2003 - journals.physiology.org
… gene encoding the cystic fibrosis transmembrane conductance … lung disease remain
uncertain. A number of mechanisms have been proposed to link the CF genotype to clinical disease

A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis

MR Knowles, NL Church, WE Waltner… - … England Journal of …, 1990 - Mass Medical Soc
… in patients with cystic fibrosis. This … disease in these patients. To study whether the inhibition
of excessive absorption of sodium might affect the course of lung disease in cystic fibrosis, …

Novel imaging techniques for cystic fibrosis lung disease

JL Goralski, NJ Stewart, JC Woods - Pediatric pulmonology, 2021 - Wiley Online Library
… Regional differences in infection and structural lung disease in infants and young
children with cystic fibrosis. J Cyst Fibros. 2019. https://doi.org/10.1016/j.jcf.2019.10.018 34. …

[HTML][HTML] Targeting proteases in cystic fibrosis lung disease. Paradigms, progress, and potential

MC McKelvey, S Weldon, DF McAuley… - American Journal of …, 2020 - atsjournals.org
Cystic fibrosis (CF) is an autosomal recessive … lung disease of CF that causes the greatest
morbidity and mortality. The disease is caused by mutations of the CFTR (cystic fibrosis

Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

M Mall, BR Grubb, JR Harkema, WK O'Neal… - Nature medicine, 2004 - nature.com
… spontaneous lung disease sharing features with cystic fibrosis, … cystic fibrosis-like lung
disease and produces a model for the study of the pathogenesis and therapy of this disease

Inflammatory mediators in cystic fibrosis lung disease

M Berger - Allergy and asthma proceedings, 2002 - search.proquest.com
Cystic fibrosis (CF) is a complex multisystem disorder caused by mutations in a membrane
… and development of lung disease remains incompletely understood. Chronic lung disease, …

[HTML][HTML] Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression

LR Hoffman, HD Kulasekara, J Emerson… - … of Cystic Fibrosis, 2009 - Elsevier
BACKGROUND: Pseudomonas aeruginosa with mutations in the transcriptional regulator
LasR chronically infect the airways of people with cystic fibrosis (CF), yet the prevalence and …