… In patients with cystic fibrosis infected with P … chronic lung injury and a reduced survival.2425
Much of the knowledge of the host response in cystic fibrosis and its relation to lung injury …

… Lung disease at diagnosis in infants with cystic fibrosis … tomography in the evaluation of
cystic fibrosis lung disease. … of structural lung damage caused by cystic fibrosis, especially …

… In patients with cystic fibrosis (CF) lung damage secondary to chronic infection is the main
… of lung disease to reduce the impact of infection, inflammation and subsequent lung injury is …

… chronic lung injury but not in complete absence of lipid-raft CFTR as in ΔF508-cystic fibrosis.
In … for ΔF508-cystic fibrosis but may not be effectual in treating lung injury and emphysema. …

… either congenital or acquired conditions, including lung diseases [228,229,230]. Their
regenerative capacities towards repair of lung injuries and reduction of inflammation is likely to be …

… In the present study, we evaluated lung injury to explore the protection of CFTR on LPS-induced
ALI, by measuring inflammatory cytokines in both BALF and lung tissues, and …

… Following the discovery of the cystic fibrosis transmembrane conductance regulator (CFTR) …
Leukocyte elastase: physiological functions and role in acute lung injury. Am J Respir Crit …

… The lung parenchyma is virtually untouched … lung involvement in cystic fibrosis and
summarizes new developments on the diagnostic approach of CF and pathogenesis of related lung …

… conjunction with abnormalities in protective antioxidants, may be important mediators of
tissue damage in patients with cystic fibrosis,-7 especially of the chronic lung injury (fig 2). This …

… cystic fibrosis lung disease. We summarise the current knowledge and the methods used to
characterise and quantify early lung … and structural lung injury in children with cystic fibrosis: …