Background: Left ventricular non-compaction (LVNC) is a cardiomyopathy characterized by
prominent trabeculae and intertrabecular recesses. We present the cases of 3 girls with the …

Background Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an ion
channelopathy usually caused by gain-of-function mutations ryanodine receptor type-2 …

Discussion In this report we present a unique case with presenting with both classic CPVT
with ryanodine receptor mutation and classic morphological features of NCCM. CPVT is …

Aims Ryanodine receptor gene (RYR2) mutations are well known to cause
catecholaminergic polymorphic ventricular tachycardia (CPVT). Recently, RYR2 exon 3 …

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a highly malignant genetic
channelopathy associated with exertional syncope and reproducible polymorphic ventricular …

Background: Left ventricular non-compaction cardiomyopathy (LVNC) is a rare congenital
cardiomyopathy characterized by increased trabeculation in one or more segments of the …

Background There are limited data on ventricular arrhythmias (VAs) associated with left
ventricular noncompaction (LVNC) cardiomyopathy. Objectives This study aims to analyze …

Left ventricular non‐compaction (LVNC) is a cardiomyopathy that may be of genetic origin;
however, few data are available about the yield of mutation, the spectrum of genes and …

Background: Left ventricular noncompaction cardiomyopathy (LVNC) is a rare cardiac
disorder characterised by the presence of a two-layer myocardium with prominent …

Development. subtypes including benign LVNC with preserved systolic and diastolic
function, dilated, hypertrophic, restrictive, and arrhythmogenic LVNC. 16 The reasons for the …