Hereditary hemorrhagic telangiectasia

T Kühnel, K Wirsching, W Wohlgemuth… - … Clinics of North …, 2018 - oto.theclinics.com
The characteristic defects in the vascular wall seen in HHT lead to a selfperpetuating
process that results in the development of highly vulnerable lesions with extremely thin …

[HTML][HTML] Hereditary hemorrhagic telangiectasia: genetics, pathophysiology, diagnosis, and management

A Viteri-Noël, A González-García, JL Patier… - Journal of clinical …, 2022 - mdpi.com
Hereditary hemorrhagic telangiectasia is an inherited disease related to an alteration in
angiogenesis, manifesting as cutaneous telangiectasias and epistaxis. As complications, it …

[HTML][HTML] Surgery or No Surgery? Exploring the Dilemma of Epistaxis Management in Patients with HHT

GC Passali, M Santantonio, N Vecchioli… - Journal of Clinical …, 2024 - mdpi.com
Background: Epistaxis, particularly in Hereditary Hemorrhagic Telangiectasia (HHT)
patients, is a common otolaryngological emergency, often requiring complex management …

Surgiflo® hemostatic matrix versus NasoPore® nasal packing following postassium titanyl phosphate laser surgery for hereditary hemorrhagic telangiectasia: A …

JM Pyne, S Murray, BC Kelly, JS Song… - Laryngoscope …, 2023 - Wiley Online Library
Background To help ensure adequate hemostasis immediately following potassium titanyl
phosphate (KTP) laser treatment, many centres treating hereditary hemorrhagic …

Safety and efficacy of blue light laser treatment in hereditary hemorrhagic telangiectasia

M Bertlich, F Kashani, BG Weiss… - Lasers in Surgery …, 2021 - Wiley Online Library
Background and Objectives Hereditary hemorrhagic telangiectasia (HHT) is a hereditary
condition that is associated with arteriovenous malformations. A common site for these …

[HTML][HTML] TIMolol nasal spray as a treatment for epistaxis in hereditary hemorrhagic telangiectasia (TIM-HHT)—a prospective, randomized, double-blind, controlled …

KEC Andorfer, F Zeman, M Koller, J Zeller, R Fischer… - Pharmaceutics, 2022 - mdpi.com
To date, there is no approved local therapeutic agent for the treatment of epistaxis due to
hereditary hemorrhagic telangiectasia (HHT). Several case reports suggest the topical use …

[HTML][HTML] HHT-Related Epistaxis and Pregnancy—A Retrospective Survey and Recommendations for Management from an Otorhinolaryngology Perspective

KEC Andorfer, CT Seebauer, C Dienemann… - Journal of Clinical …, 2022 - mdpi.com
Appropriate management of hereditary hemorrhagic telangiectasia (HHT) is of particular
importance in females, as HHT-mediated modifications of the vascular bed and circulation …

[HTML][HTML] Hereditary hemorrhagic telangiectasia: success of the Osler calendar for documentation of treatment and course of disease

CT Seebauer, V Freigang, FE Schwan… - Journal of Clinical …, 2021 - mdpi.com
Hereditary hemorrhagic telangiectasia (HHT; Rendu-Osler-Weber syndrome) affects the
capillary and larger vessels, leading to arteriovenous shunts. Epistaxis is the main symptom …

[HTML][HTML] Silicone septal splint for recurrent epistaxis in HHT patients: experience of a national referral centre

E Matti, E Maiorano, B Nacu, A Luceri… - Acta …, 2023 - ncbi.nlm.nih.gov
Objective To report our experience in the use of silicone septal splint for recurrent severe
epistaxis in hereditary haemorrhagic telangiectasia patients (HHT). Methods This is a …

Influence of temporary nasal occlusion (tNO) on epistaxis frequency in patients with hereditary hemorrhagic telangiectasia (HHT)

KEC Wirsching, F Haubner, TS Kühnel - European Archives of Oto-Rhino …, 2017 - Springer
The objective of the study was to evaluate the influence of temporary nasal occlusion (tNO)
with hypoallergenic tape on the frequency and severity of epistaxis in patients with …