Respiratory failure in amyotrophic lateral sclerosis

S Niedermeyer, M Murn, PJ Choi - Chest, 2019 - Elsevier
Amyotrophic lateral sclerosis is a progressive neuromuscular disease characterized by both
lower motor neuron and upper motor neuron dysfunction. Although clinical presentations …

Communication matters—pitfalls and promise of hightech communication devices in palliative care of severely physically disabled patients with amyotrophic lateral …

K Linse, E Aust, M Joos, A Hermann - Frontiers in neurology, 2018 - frontiersin.org
Amyotrophic lateral sclerosis (ALS) is the most common motor neuron disease, leading to
progressive paralysis, dysarthria, dysphagia, and respiratory disabilities. Therapy is mostly …

Canadian best practice recommendations for the management of amyotrophic lateral sclerosis

C Shoesmith, A Abrahao, T Benstead, M Chum… - Cmaj, 2020 - Can Med Assoc
The care and management of patients with ALS should always be patient focused, with
attention to holistic and emotional aspects of well-being. It is the patient who ultimately …

Non‐invasive and tracheostomy invasive ventilation in amyotrophic lateral sclerosis: utilization and survival rates in a cohort study over 12 years in Germany

S Spittel, A Maier, D Kettemann… - European Journal of …, 2021 - Wiley Online Library
Background and purpose The aim of this study was to investigate utilization rates, treatment
pathways and survival prognosis in patients with amyotrophic lateral sclerosis (ALS) …

Attitudes towards hastened death in ALS: a prospective study of patients and family caregivers

R Stutzki, M Weber, S Reiter-Theil… - … Lateral Sclerosis and …, 2014 - Taylor & Francis
Amyotrophic lateral sclerosis (ALS) may be associated with the wish to hasten death
(WTHD). We aimed to determine the prevalence and stability of WTHD and end-of-life …

Palliative care principles in ALS

C Shoesmith - Handbook of clinical neurology, 2023 - Elsevier
Amyotrophic lateral sclerosis (ALS) is a progressive neurodegenerative disease associated
with progressive dysphagia, dysarthria, extremity weakness, and dyspnea. Although there …

Practical guide to management of long-term noninvasive ventilation for adults with chronic neuromuscular disease

J Hansen-Flaschen, J Ackrivo - Respiratory Care, 2023 - rc.rcjournal.com
Recent technological advances in respiratory support and monitoring have dramatically
enhanced the utility of long-term noninvasive ventilation (NIV). Improved quality of life and …

Symptom management and end-of-life care in amyotrophic lateral sclerosis

CE Jackson, AL McVey, S Rudnicki… - Neurologic …, 2015 - neurologic.theclinics.com
Sialorrhea should initially be treated with anticholinergic medications. For patients who
remain medically refractory, treatment with botulinum toxin type B (level B; recommendation …

Advance care planning in motor neuron disease: A systematic review

L Murray, PN Butow - Palliative & supportive care, 2016 - cambridge.org
Objective: Motor neuron disease (MND) is an incurable progressive illness, characterized by
incessant deterioration of neuromuscular function. Timely commencement of advance care …

The experiences of patients with amyotrophic lateral sclerosis of their decision‐making processes to invasive home mechanical ventilation—A qualitative study

T Thorborg, J Finderup, DS Winther… - Nursing …, 2023 - Wiley Online Library
Aim To explore and gain knowledge of the experiences and needs among patients with
amyotrophic lateral sclerosis (ALS) of their decision‐making processes whether to choose …