In this scientific statement from the American Heart Association, experts in the field of
cardiomyopathy (heart muscle disease) in children address 2 issues: the most current …

Left ventricular hypertrabeculation (LVHT) or noncompaction is a myocardial abnormality of
unknown aetiology, frequently associated with monogenic disorders, particularly …

Non-compaction of the left ventricular myocardium (LVNC) has gained increasing
recognition during the last 25 years. There is a morphological trait of the myocardial …

Inherited cardiomyopathies include hypertrophic cardiomyopathy, dilated cardiomyopathy,
arrhythmogenic right ventricular cardiomyopathy, left ventricular noncompaction, and …

Background—Left ventricular noncompaction (LVNC) is a genetically and phenotypically
heterogeneous disease and, although increasingly recognized in clinical practice, there is a …

Aims In this study, we aimed to clinically and genetically characterize LVNC patients and
investigate the prevalence of variants in known and novel LVNC disease genes. Introduction …

Background A genetic cause can be identified in 30% of noncompaction cardiomyopathy
patients (NCCM) with clinical features ranging from asymptomatic cardiomyopathy to heart …

Background Left ventricular hypertrabeculation (LVHT), also known as noncompaction or
spongy myocardium, is a cardiac abnormality of unknown etiology and pathogenesis …

Isolated left ventricular noncompaction (ILVNC) is a cardiomyopathy that was first described
in 1926 as a “spongy myocardium.” The disorder results from intrauterine arrest of …

Ventricular trabeculation and compaction are two of the many essential steps for generating
a functionally competent ventricular wall. A significant reduction in trabeculation is usually …