BACKGROUND Hepatic steatosis is a common form of cystic fibrosis associated liver
disease (CFLD) seen in an estimated 15%-60% of patients with cystic fibrosis (CF). The …

In developed countries, it is projected that there will be a 70% increase in the number of
adults living with Cystic Fibrosis (CF) between 2010 and 2025. This shift in demographics …

Multiple organ systems, including the gastrointestinal tract, pancreas, and hepatobiliary
systems, are affected by cystic fibrosis (CF). Many of these changes begin early in life and …

Gastrointestinal (GI) abnormalities are integral to the clinical manifestations of cystic fibrosis
(CF). Indeed, the very first publication of CF in 1938 reported pediatric steatorrhea with …

Background Cystic fibrosis‐related liver disease (CFLD) is the leading cause of death in
cystic fibrosis (CF), after pulmonary disease. To improve identification and management of …

Cystic fibrosis (CF) is the most common lethal autosomal recessive disease in the white
population. Mutation of the CF transmembrane conductance regulator gene on chromosome …

Cystic fibrosis (CF) is an autosomal recessive disorder caused by mutations in the CF
transmembrane conductance regulator gene. CF liver disease develops in 5%-10% of …

Educational aims The reader will come to appreciate that: Severe cystic fibrosis liver disease
(CLFD) commonly presents in early childhood years, and affects up to 10% of people with …

Objectives: The aim of the study was to evaluate whether liver stiffness measurement (LSM),
determined by transient elastography, correlates with presence and severity of liver disease …

AIM To investigate the clinical, biochemical and imaging characteristics of adult cystic
fibrosis (CF) patients with hepatic steatosis as compared to normal CF controls. METHODS …