Methods to identify children with cystic fibrosis (CF) at risk for development of advanced liver
disease are lacking. We aim to determine the association between liver stiffness …

Objectives: The aims of the study were to determine the frequency of hepatobiliary disease
in patients with cystic fibrosis and to describe the sociodemographic, clinical, and laboratory …

Objectives: Cystic fibrosis-related liver disease (CFLD) with consecutive cirrhosis is the third
most common cause of death in CF patients. The aim of this study was to identify the …

Abstract Background and Aims Early identification of risk factors for the development of
severe fibrosis in children with cystic fibrosis‐related liver disease (CFLD) is crucial as …

Cystic fibrosis (CF) is an autosomal recessive disease characterized by mutations in the
gene that encodes for the cystic fibrosis transmembrane conductance regulator protein …

Background. Complications of cystic fibrosis‐associated liver disease (CFLD) are a leading
nonpulmonary cause of death. Noninvasive tests enabling early detection of liver changes …

Current recommendations [1, 2] for screening of cystic fibrosis liver disease (CFLD) in
people with cystic fibrosis (CF) include liver biochemistries, complete blood count and …

Background Hepatic steatosis is a common manifestation of CF-related liver disease
(CFLD). Controlled attenuation parameter (CAP) measurement during transient …

Objectives: Systematic study of allograft liver histology in children undergoing orthotopic
liver transplantation (LT) for cystic fibrosis-related liver disease (CFLD). Methods …

Background Cystic fibrosis associated liver disease (CFLD) carries a significant disease
burden with no effective preventive therapies. According to the gut-liver axis hypothesis for …