[HTML][HTML] Alterations in the fecal microbiota in patients with advanced cystic fibrosis liver disease after 6 months of elexacaftor/tezacaftor/ivacaftor

JT Duong, CE Pope, HS Hayden, C Miller… - Journal of Cystic …, 2024 - Elsevier
Background Cystic fibrosis associated liver disease (CFLD) carries a significant disease
burden with no effective preventive therapies. According to the gut-liver axis hypothesis for …

Hepatic enzyme ALT as a marker of glucose abnormality in men with cystic fibrosis

J Colomba, SR Netedu, C Lehoux-Dubois, A Coriati… - PLoS …, 2019 - journals.plos.org
Aim Cystic fibrosis (CF) patients are at high risk of developing CF-related diabetes (CFRD).
In non-CF patients, liver disease, specifically steatosis and non-alcoholic fatty liver disease …

The changing face of cystic fibrosis: an update for anesthesiologists

AJ Lee, JL Huffmyer, EL Thiele, PL Zeitlin… - Anesthesia & …, 2022 - journals.lww.com
Cystic fibrosis (CF) is the most common fatal genetic disease in North America. While CF is
more common among Whites, it is increasingly being recognized in other races and …

Activated L-arginine/nitric oxide pathway in pediatric cystic fibrosis and its association with pancreatic insufficiency, liver involvement and nourishment: an overview …

F Brinkmann, B Hanusch, M Ballmann… - Journal of Clinical …, 2020 - mdpi.com
Cystic fibrosis (CF; OMIM 219700) is a rare genetic disorder caused by a chloride channel
defect, resulting in lung disease, pancreas insufficiency and liver impairment. Altered L …

Pathologic features of hereditary cholestatic diseases

AD Clouston - Surgical Pathology Clinics, 2018 - surgpath.theclinics.com
The inherited diseases causing conjugated hyperbilirubinemia are diverse, with variability in
clinical severity, histologic appearance, and time of onset. The liver biopsy appearances can …

Factors associated with frequent high-cost individuals with cystic fibrosis and their healthcare utilization and cost patterns

S Desai, W Zhang, JM Sutherland, J Singer… - Scientific Reports, 2023 - nature.com
Cystic fibrosis (CF) is a progressive multi-organ disease with significant morbidity placing
extensive demands on the healthcare system. Little is known about those individuals with …

[HTML][HTML] Advanced but not mild liver disease is a predictor of decreased survival in children with cystic fibrosis, with far greater impact in females: A 27-year real-life …

M Baldissera, PJ Lewindon, LE Ramm, GF Hartel… - Journal of Cystic …, 2022 - Elsevier
Background Improved survival of children with CF has increased our need to understand the
relevance of cystic fibrosis-associated liver disease (CFLD). We assessed the impact of liver …

Pancreas transplantation for cystic fibrosis: a frequently missed opportunity

JA Fridell, MA Bozic, BJ Ulrich, AJ Lutz… - Clinical …, 2021 - Wiley Online Library
Cystic fibrosis (CF) is an inherited autosomal recessive disorder. Despite optimized therapy,
the majority of affected individuals ultimately die of respiratory failure. As patients with CF …

[PDF][PDF] Inflammation, Fibrosis and Cancer: Mechanisms, Therapeutic Options and Challenges. Cancers 2022, 14, 552

B Wu, QH Sodji, AK Oyelere - 2022 - researchgate.net
Uncontrolled inflammation is a salient factor in multiple chronic inflammatory diseases and
cancers. In this review, we provided an in-depth analysis of the relationships and distinctions …

Capillary electromigration techniques as tools for assessing the status of vitamins A, C and E in patients with cystic fibrosis

I Olędzka, K Kaźmierska, A Plenis, B Kamińska… - … of Pharmaceutical and …, 2015 - Elsevier
The purpose of this work is the evaluation of the nutritional status of patients with cystic
fibrosis (CF), based on the level of vitamin C in urine and vitamins A and E in serum, using …