Pulmonary hypertension in chronic lung diseases

W Seeger, Y Adir, JA Barberà, H Champion… - Journal of the American …, 2013 - jacc.org
Chronic obstructive lung disease (COPD) and diffuse parenchymal lung diseases (DPLD),
including idiopathic pulmonary fibrosis (IPF) and sarcoidosis, are associated with a high …

Idiopathic pulmonary fibrosis beyond the lung: understanding disease mechanisms to improve diagnosis and management

F Luppi, M Kalluri, P Faverio, M Kreuter, G Ferrara - Respiratory Research, 2021 - Springer
Idiopathic pulmonary fibrosis (IPF) is a chronic and progressive disorder with an estimated
median survival time of 3–5 years after diagnosis. This condition occurs primarily in elderly …

Clinical course and prediction of survival in idiopathic pulmonary fibrosis

B Ley, HR Collard, TE King Jr - American journal of respiratory and …, 2011 - atsjournals.org
Idiopathic pulmonary fibrosis (IPF) is a progressive, life-threatening, interstitial lung disease
of unknown etiology. The median survival of patients with IPF is only 2 to 3 years, yet some …

Incidence and prevalence of idiopathic pulmonary fibrosis: review of the literature

L Nalysnyk, J Cid-Ruzafa, P Rotella… - European Respiratory …, 2012 - Eur Respiratory Soc
Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, fibrosing interstitial pneumonia
of unknown aetiology. It is a rare disease, and its incidence and prevalence are not clear …

Idiopathic pulmonary fibrosis

TE King, A Pardo, M Selman - The Lancet, 2011 - thelancet.com
Idiopathic pulmonary fibrosis is a devastating, age-related lung disease of unknown cause
that has few treatment options. This disease was once thought to be a chronic inflammatory …

ASPIRE registry: assessing the Spectrum of Pulmonary hypertension Identified at a REferral centre

J Hurdman, R Condliffe, CA Elliot… - European …, 2012 - Eur Respiratory Soc
Pulmonary hypertension (PH) is a heterogeneous condition. To date, no registry data exists
reflecting the spectrum of disease across the five diagnostic groups encountered in a …

Pulmonary hypertension associated with lung disease: new insights into pathomechanisms, diagnosis, and management

KM Olsson, TJ Corte, JC Kamp, D Montani… - The Lancet …, 2023 - thelancet.com
Patients with chronic lung diseases, particularly interstitial lung disease and chronic
obstructive pulmonary disease, frequently develop pulmonary hypertension, which results in …

Guidelines for the treatment of pulmonary hypertension (JCS 2017/JPCPHS 2017)

K Fukuda, H Date, S Doi, Y Fukumoto… - Circulation …, 2019 - jstage.jst.go.jp
Pulmonary hypertension remained an unexplained intractable disease with poor prognosis.
In the last 2 decades, however, the diagnosis and treatment methods for this disease …

Premature lung aging and cellular senescence in the pathogenesis of idiopathic pulmonary fibrosis and COPD/emphysema

M Chilosi, A Carloni, A Rossi, V Poletti - Translational Research, 2013 - Elsevier
Different anatomic and physiological changes occur in the lung of aging people that can
affect pulmonary functions, and different pulmonary diseases, including deadly diseases …

Combined pulmonary fibrosis and emphysema syndrome: a review

MD Jankowich, SIS Rounds - Chest, 2012 - Elsevier
There is increasing clinical, radiologic, and pathologic recognition of the coexistence of
emphysema and pulmonary fibrosis in the same patient, resulting in a clinical syndrome …