Current therapy for hypoplastic left heart syndrome and related single ventricle lesions

RG Ohye, D Schranz, Y D'Udekem - Circulation, 2016 - Am Heart Assoc
Universally fatal only 4 decades ago, the progress in the 3-stage palliation of hypoplastic left
heart syndrome and related single right ventricular lesions has drastically improved the …

Meta-analysis of the effectiveness of heart transplantation in patients with a failing Fontan

N Tabarsi, M Guan, J Simmonds, M Toma… - The American journal of …, 2017 - Elsevier
The Fontan procedure is increasingly being used to palliate univentricular physiology. It is a
complex anatomic and physiologic repair that can fail at any age, often leaving heart …

Three decades later: The fate of the population of patients who underwent the Atriopulmonary Fontan procedure

CL Poh, D Zannino, RG Weintraub, DS Winlaw… - International journal of …, 2017 - Elsevier
Objective To review our experience of patients with an atrio-pulmonary Fontan circulation to
determine their long-term outcomes. Methods and results A retrospective analysis of long …

[HTML][HTML] Transplantation in the single ventricle population

LA Kenny, F DeRita, M Nassar, J Dark… - Annals of …, 2018 - ncbi.nlm.nih.gov
The single ventricle patient population comprises the most complex cohort presenting to the
cardiac transplant team, in terms of demographics, anatomic substrate, and unique …

Heart transplantation after Fontan operation

IE Konstantinov, A Schulz, E Buratto - JTCVS techniques, 2022 - jtcvstechniques.org
There is an increasing number of long-term survivors with complex congenital heart disease
(CHD) and single ventricle palliation, adding to a growing cohort of patients with a Fontan …

[HTML][HTML] Pre-and post-operative determinants of transplantation-free survival after Fontan. The Australia and New Zealand experience

CL Poh, RL Cordina, AJ Iyengar, D Zannino… - IJC Heart & …, 2021 - Elsevier
Background This review identifies the predictors of late mortality and heart transplantation
that remain relevant in the contemporary population of patients with a Fontan circulation …

Heart transplantation in Fontan patients across Australia and New Zealand

WY Shi, MS Yong, DC McGiffin, P Jain, PN Ruygrok… - Heart, 2016 - heart.bmj.com
Objective Patients with Fontan physiology may eventually require heart transplantation (HT).
We determined the rates and outcomes of HT in a national, population-based multicentre …

[HTML][HTML] Neonatal heart transplantation

M John, LL Bailey - Annals of cardiothoracic surgery, 2018 - ncbi.nlm.nih.gov
Neonatal heart transplantation was developed and established in the 1980's as a durable
modality of therapy for complex-uncorrectable heart disease. Patients transplanted in the …

Failures of the Fontan system in univentricular hearts and mortality risk in heart transplantation: a systematic review and meta-analysis

H Marquez-Gonzalez, JG Hernandez-Vasquez… - Life, 2021 - mdpi.com
The Fontan procedure (FP) is the standard surgical treatment for Univentricular heart
diseases. Over time, the Fontan system fails, leading to pathologies such as protein-losing …

Ten-year outcomes of Fontan conversion in Australia and New Zealand demonstrate the superiority of a strategy of early conversion

CL Poh, A Cochrane, JC Galati… - European Journal of …, 2016 - academic.oup.com
OBJECTIVE To investigate the benefits of a strategy of early Fontan conversion. METHODS
Using the Australia and New Zealand Fontan Registry, retrospective analysis of their long …