[HTML][HTML] Pleuroparenchymal fibroelastosis: clinical, radiological and histopathological features

J Ricoy, J Suárez-Antelo, J Antúnez, AM de Alegría… - Respiratory …, 2022 - Elsevier
Pleuroparenchymal fibroelastosis (PPFE) is a rare, generally idiopathic form of interstitial
pneumonia with unique clinical, radiological and histopathological features. It is named after …

[HTML][HTML] A proposed prognostic prediction score for pleuroparenchymal fibroelastosis

Y Kinoshita, T Ikeda, T Miyamura, Y Ueda… - Respiratory …, 2021 - Springer
Background Clinical course of pleuroparenchymal fibroelastosis (PPFE) shows
considerable variation among patients, but there is no established prognostic prediction …

Pleuroparenchymal Fibroelastosis (PPFE)—An Update

P Evans - Current Pulmonology Reports, 2023 - Springer
Abstract Purpose of Review This review highlights the clinical, radiological and histological
features of pleuroparenchymal fibroelastosis (PPFE) as well as the typical disease course …

Platythorax progresses with lung involvement in pleuroparenchymal fibroelastosis

T Ikeda, Y Kinoshita, T Miyamura, Y Ueda… - Respiratory …, 2022 - Elsevier
Background Patients diagnosed with pleuroparenchymal fibroelastosis (PPFE) exhibit
unique clinical features, including upper lobe-dominant lung involvement and platythorax (or …

Platythorax increases residual volume/total lung capacity in idiopathic pleuroparenchymal fibroelastosis

Y Kinoshita, S Takenaka, K Takata… - ERJ Open …, 2024 - Eur Respiratory Soc
CT: computed tomography, DLCO: diffusion capacity for carbon monoxide, FEV1: forced
expiratory volume in 1 second, FVC: forced vital capacity, ILD: interstitial lung disease …

Clinical, radiological and pathological features of idiopathic and secondary interstitial pneumonia with pleuroparenchymal fibroelastosis in patients undergoing lung …

N Ikegami, N Nakajima, A Yoshizawa, T Handa… - …, 2022 - Wiley Online Library
Aims Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare type of idiopathic
interstitial pneumonia, and pathological PPFE is also observed in patients with secondary …

Partial pressure of carbon dioxide levels reflect disease severity in idiopathic pleuroparenchymal fibroelastosis

Y Kinoshita, T Utsunomiya, Y Koide, K Wada… - Respiratory …, 2023 - Elsevier
Background Hypercapnia can cause a disturbance of consciousness and adversely affect a
patient's general condition. Patients with interstitial lung disease seldom experience …

[HTML][HTML] Severe and progressive platythorax disproportionate to lung fibrosis: a rare variant of idiopathic pleuroparenchymal fibroelastosis

T Ikeda, Y Kinoshita, Y Ueda, T Sasaki… - … Medicine Case Reports, 2021 - Elsevier
A 57-year-old man was referred to our department because of progressive shortness of
breath and emaciation. He had experienced pneumothorax three times in the past five …

[PDF][PDF] Clinical, radiological, and pathological features of idiopathic and secondary interstitial pneumonia cases with pleuroparenchymal fibroelastosis undergoing lung …

N Ikegami - 2022 - repository.kulib.kyoto-u.ac.jp
Aims: Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare type of idiopathic
interstitial pneumonia, and pathological PPFE is also observed in secondary interstitial …