PURPOSE OF REVIEW This article details updated clinical presentations and current
treatment paradigms of the common otologic disorders that may present to the neurologist …

1958 年Lehnhardt [1] 首次描述了进行性双侧感音神经性听力损失(sensorineuralhearingloss,
SNHL) 患者的抗原抗体反应, 推测双耳突聋的病因可能是一种免疫反应. 1979 年, McCabe …

Cogan syndrome (CS) is a rare vasculitis seen primarily in young adults. It predominantly
affects eyes, ears and the heart with characteristic findings of interstitial keratitis …

Abstract Background Rare diseases (RDs) affect less than 5/10,000 people in Europe and
fewer than 200,000 individuals in the United States. In rheumatology, RDs are …

Objective Cogan's syndrome (CS) is an inflammatory disease classified as variable vessel
vasculitis. It is a rare disease with few published series, and therefore we reviewed our …

Vasculitis refers to heterogeneous clinicopathologic disorders that share the histopathology
of inflammation of blood vessels. Unrecognized and therefore untreated, vasculitis of the …

Patients with hearing loss depend more on their vision on their communication and vice
versa. ENT physician faces difficult situation when he or she consults a patient complaining …

A 61-year-old man presented with weight loss, bilateral ocular redness, blurred vision, and
sensorineural hearing loss. Fluorodeoxyglucose-position emission tomography/computed …

Cogan's syndrome (CS) is a rare autoimmune disease in which approximately 10%–13% of
people with the condition develop neurological symptoms. While glucocorticoids are the …

Background Cogan's syndrome is a rare disorder of unknown origin characterized by
inflammatory ocular disease and vestibuloauditory symptoms. Systemic vasculitis is found in …