Background Neurofibromatosis of types 1 and 2 (NF1, NF2) and schwannomatosis are the
diseases that make up the neurofibromatosis spectrum. With respective incidences of 1 in …

Neurofibromatosis (NF) encompasses a group of distinct genetic disorders in which affected
children and adults are prone to the development of benign and malignant tumors of the …

Vestibular schwannoma (VS) is a benign tumour arising from the vestibular component of
the vestibulocochlear nerve. Treatment protocols range from observation to microsurgical …

Vestibular schwannomas (VS) expand slowly in the internal auditory canal, in the
cerebellopontine angle, inside the cochlear and the labyrinth. Larger tumors can displace …

Neurofibromatosis (NF) is one of the most common genetic disorders. Inherited in an
autosomal dominant fashion, this phacomatosis is classified into two genetically distinct …

Abstract Neurofibromatosis type 2 (NF2) is an autosomal dominant inherited tumor
predisposition syndrome caused by mutations in the NF2 gene on chromosome 22. Affected …

BACKGROUND: Single-session stereotactic radiosurgery (SRS) treatment of vestibular
schwannomas results in excellent tumor control. It is not known whether functional outcomes …

BACKGROUND: Management of neurofibromatosis type 2 (NF2)—associated vestibular
schwannomas (VSs) remains controversial. Stereotactic radiosurgery (SRS) with …

Abstract Background Neurofibromatosis type 2 (NF2) is a tumor syndrome that results from
mutation of the NF2 tumor suppressor gene. The hallmark of NF2 is the presence of bilateral …

Abstract Introduction Neurofibromatosis type 2 (NF2) is characterized by often bilateral
vestibular schwannomas (VS) that result in progressive hearing loss and compression of …