British Society for Rheumatology guideline on management of paediatric, adolescent and adult patients with idiopathic inflammatory myopathy

AGS Oldroyd, JB Lilleker, T Amin, O Aragon… - …, 2022 - academic.oup.com
Background Idiopathic inflammatory myopathy (IIM) is a multi-system autoimmune condition
characterised by muscle inflammation (myositis), interstitial lung disease (ILD), and skin …

Measures of adult and juvenile dermatomyositis, polymyositis, and inclusion body myositis: physician and patient/parent global activity, manual muscle testing (mmt) …

LG Rider, VP Werth, AM Huber… - Arthritis care & …, 2011 - Wiley Online Library
The idiopathic inflammatory myopathies, including adult and juvenile dermatomyositis (DM),
polymyositis (PM), and inclusion body myositis (IBM), are rare systemic autoimmune …

2016 American College of Rheumatology/European League Against Rheumatism criteria for minimal, moderate, and major clinical response in adult dermatomyositis …

R Aggarwal, LG Rider, N Ruperto… - Arthritis & …, 2017 - Wiley Online Library
Objective To develop response criteria for adult dermatomyositis (DM) and polymyositis
(PM). Methods Expert surveys, logistic regression, and conjoint analysis were used to …

Clinical outcome measures in juvenile idiopathic arthritis

A Consolaro, G Giancane, B Schiappapietra… - Pediatric …, 2016 - Springer
Juvenile idiopathic arthritis (JIA), as a chronic condition, is associated with significant
disease-and treatment-related morbidity, thus impacting children's quality of life. In order to …

Update on outcome assessment in myositis

LG Rider, R Aggarwal, PM Machado… - Nature Reviews …, 2018 - nature.com
The adult and juvenile myositis syndromes, commonly referred to collectively as idiopathic
inflammatory myopathies (IIMs), are systemic autoimmune diseases with the hallmarks of …

Juvenile idiopathic inflammatory myositis: an update on pathophysiology and clinical care

C Papadopoulou, C Chew, MGL Wilkinson… - Nature Reviews …, 2023 - nature.com
The childhood-onset or juvenile idiopathic inflammatory myopathies (JIIMs) are a
heterogenous group of rare and serious autoimmune diseases of children and young …

Juvenile dermatomyositis. Where are we now?

LJ McCann, P Livermore, MGL Wilkinson… - Clinical and …, 2022 - discovery.ucl.ac.uk
Juvenile onset idiopathic inflammatory myopathy (IIM) has many similarities and distinct
differences from adult-onset disease. This review will focus on recent developments in …

The PRINTO criteria for clinically inactive disease in juvenile dermatomyositis

D Lazarevic, A Pistorio, E Palmisani… - Annals of the …, 2013 - ard.bmj.com
Objectives To develop data-driven criteria for clinically inactive disease on and off therapy
for juvenile dermatomyositis (JDM). Methods The Paediatric Rheumatology International …

Juvenile dermatomyositis: new developments in pathogenesis, assessment and treatment

LR Wedderburn, LG Rider - Best practice & research Clinical rheumatology, 2009 - Elsevier
Juvenile dermatomyositis (JDM) is a rare, potentially life-threatening systemic autoimmune
disease primarily affecting muscle and skin. Recent advances in the recognition …

Improvement in disease activity in refractory juvenile dermatomyositis following abatacept therapy

RV Curiel, W Nguyen, G Mamyrova… - Arthritis & …, 2023 - Wiley Online Library
Objective This open‐label, 24‐week study was conducted to evaluate the safety and efficacy
of abatacept in patients with refractory juvenile dermatomyositis (DM). Methods Ten …