Idiopathic interstitial fibrosis has nonspecific, insidious clinical symptoms; it is the most
common interstitial disease and has the worse known prognosis, with a survival without …

Pleuroparenchymal fibroelastosis (PPFE) is a rare lung disease with unprecedented
features characterized by fibroelastotic changes in the subpleural lung parenchyma affecting …

Aims Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare type of idiopathic
interstitial pneumonia, and pathological PPFE is also observed in patients with secondary …

Background: Pleuroparenchymal Fibroelastosis (PPFE) is a rare disease that consists of
elastofibrosis that involves the pleura and subpleural lung parenchyma; it is an unusual …

Idiopathic pleuroparenchymal fibroelastosis (iPPFE) is a rare form of idiopathic interstitial
pneumonia. We report a case of a patient with iPPFE in whom postural changes improved …

Background Hypercapnia can cause a disturbance of consciousness and adversely affect a
patient's general condition. Patients with interstitial lung disease seldom experience …

Airway-centered fibroelastosis is characterized by peribronchovascular fibroelastosis,
predominantly in the upper lobes, with little-to-no pleural involvement. In this study, we …

In this article, we report a case with pleuroparenchymal fibroelastosis (PPFE) following
hematopoietic stem cell transplantation (HSCT) that developed acute respiratory failure with …

The term idiopathic pleuroparenchymal fibroelastosis refers to a rare interstitial lung disease
that predominantly involves the upper lobes. It has been considered a rare subtype of …

Pleuroparenchymal fibroelastosis (PPFE) is a relatively rare interstitial lung disease (ILD)
consisting of elastofibrosis involving the subpleural parenchyma and visceral pleura with an …