Rationale: The 2002 American Thoracic Society/European Respiratory Society classification
of idiopathic interstitial pneumonias identified nonspecific interstitial pneumonia (NSIP) as a …

The lung is frequently involved in connective tissue diseases (CTDs), although the
frequency of lung manifestations varies according to the type of CTD. Interstitial lung …

Rationale: Clinicopathologic pulmonary manifestations associated with primary Sjögren's
syndrome have yet to be reviewed in a large series since the recognition of nonspecific …

PURPOSE: To evaluate computed tomographic (CT) patterns of lung disease in patients
with systemic sclerosis (SSc) and compare them with CT appearance in patients with biopsy …

INTRODUCTION: Few data are available on the epidemiology of interstitial lung diseases
(ILDs), especially after the current classification of idiopathic interstitial pneumonias. The aim …

1. INTRODUCTION 1.1 An overview of the ILD guideline Since the publication of the first
BTS guidelines for diffuse lung disease nearly 10years ago, 1 the specialty has seen …

Aims and methods: Pulmonary parenchymal disease is common in patients with connective
tissue disorders (CTDs). However, most reports precede recognition of non‐specific …

Studies using genetically modified mice have revealed fundamental functions of the
transcription factor Fos/AP-1 in bone biology, inflammation, and cancer. However, the …

Idiopathic pulmonary fibrosis (IPF) is the most common and lethal form of idiopathic
interstitial pneumonia. The disease, which occurs primarily in middle-aged and older adults …

The connective tissue disorders (CTDs), also called collagen vascular diseases (CVDs),
represent a heterogeneous group of immunologically mediated inflammatory disorders with …