Left ventricular hypertrabeculation (LVHT) or noncompaction is a myocardial abnormality of
unknown aetiology, frequently associated with monogenic disorders, particularly …

Muscular dystrophy (MD) connotes a heterogeneous group of inherited disorders
characterized by progressive wasting and weakness of the skeletal muscles. In several …

Background Left ventricular hypertrabeculation (LVHT), also known as noncompaction or
spongy myocardium, is a cardiac abnormality of unknown etiology and pathogenesis …

In contrast with Steinert's disease (DM1), type 2 muscular dystrophy (DM2) is not known to
be associated with a high prevalence of cardiac involvement. Our objective was to compare …

Introduction: When> 3 trabeculations associated with interventricular recesses are found,
this is termed 'left ventricular hypertrabeculation/noncompaction'(LVHT). Cardiac-imaging …

Arrhythmias in left ventricular hypertrabeculation/noncompaction (LVHT) comprise sustained
or non-sustained ventricular tachycardia (VT)(n= 135), atrial fibrillation (AF)(n= 96) AV block …

The link between heart and skeletal muscle disorders is based on similar molecular,
anatomical and clinical features, which are shared by the 'primary'cardiomyopathies and …

Little is known regarding cardiac involvement (CI) by neuromuscular disorders (NMDs). The
purpose of this review is to summarise and discuss the major findings concerning the types …

Left ventricular hypertrabeculation/noncompaction (LVHT) is in the majority of the cases
associated with hereditary cardiac or skeletal muscle disease or with chromosomal …

Abstract Myotonic dystrophy type 2 (DM2) is a genetically distinct disorder that shares some
phenotypical features of myotonic dystrophy type 1 (DM1). However, anesthetic …