IgG4-related sclerosing cholangitis (IgG4-SC) is often associated with autoimmune
pancreatitis. However, the diffuse cholangiographic abnormalities observed in IgG4-SC may …

Introduction Immunoglobulin G4-related disease (IgG4-RD) is a debilitating multiorgan
disease characterized by recurring flares leading to organ dysfunction, decreased quality of …

Background Type 1 autoimmune pancreatitis (AIP), as a pancreatic manifestation of IgG4-
related disease, shows a favorable prognosis in the short term. However, disease relapse is …

IgG4-related systemic disease (IgG4-RSD) is an emerging clinical entity about which much
remains to be elucidated, in terms of its aetiology, pathogenesis, diagnosis, treatment and …

Objectives: It is of utmost importance that autoimmune pancreatitis (AIP) be differentiated
from pancreatic cancer (PC) because some AIP cases undergo unnecessary laparotomy or …

The term cholestasis is derived from the Greek word “chole,” which means bile, and “stasis,”
meaning standing still. Cholestasis develops either from a defect in bile synthesis …

Retroperitoneal fibrosis (RPF) is a rare disease characterized by chronic, nonspecific
inflammatory and sclerotic or fibrotic tissue in the periaortic or periiliac retroperitoneum that …

Objectives: IgG4-associated systemic disease (ISD) is a multiorgan fibroinflammatory
disorder whose pancreatic manifestation is called autoimmune pancreatitis (AIP). We …

Objectives The risk of pancreatic and extrapancreatic cancer in autoimmune pancreatitis
(AIP) has not been systematically evaluated. We compared the risk of malignancy in AIP …

Purpose: To review the current state of knowledge of IgG4-related ophthalmic disease (IgG4-
ROD). Methods: A review of the literature and personal experience of the authors. Results …