Patients with Marfan syndrome (MFS), a connective tissue disorder caused by pathogenic
variants in the gene encoding the extracellular matrix protein fibrillin-1, have an increased …

Öz Noncompaction cardiomyopathy is a novel cardiomyopathy type which is manifested by
heart failure, thromboembolic events, arrhythmias and sudden cardiac death. This cardiac …

Background Left ventricular noncompaction is associated with arrhythmias. The indication
for implantation of devices for primary prophylaxis of sudden cardiac death in …

Objective: Left ventricular non-compaction is a rare cardiomyopathy following an early arrest
in endomyocardial morphogenesis. This study aimed to present the clinical and …

Noncompaction cardiomyopathy (NCCM) was first described almost a half century ago, it
initially began as an unusual autopsy finding. NCCM has a highly variable clinical …

Left ventricular hypertrabeculation (LVHT) is frequently associated with neuromuscular
disorders (NMDs) but in the vast majority of the cases the NMD is hereditary [1]. Acquired …

Background Noncompaction cardiomyopathy (NCM) stands as a rare hereditary cardiac
disorder intricately linked to adverse cardiovascular events, including heart failure …

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy, with still not universally
accepted diagnostic criteria and a paucity of data regarding its detailed pathogenesis …

Distinguishing congenital long QT syndrome from QT prolongation caused by drugs or a
different underlying disease process is essential for selecting the proper treatment. Herein …

Некомпактный миокард ассоциируется с развитием сердечной недостаточности и
различных аритмий. Каких-либо характерных для некомпактного миокарда аритмий …