Clinical–radiological–pathological correlation in pulmonary hypertension with unclear and/or multifactorial mechanisms

M Lichtblau, L Mayer, D Gopalan… - European …, 2023 - Eur Respiratory Soc
Ever since the second world symposium on pulmonary hypertension (PH) held in Evian,
France, in 1998, PH has been classified into five major clinical groups. Group 5 PH includes …

Pulmonary hypertension in connective tissue diseases: epidemiology, pathogenesis, and treatment

DÜ Cansu, C Korkmaz - Clinical Rheumatology, 2023 - Springer
Pulmonary hypertension (PH) is a clinical condition characterized by increased pulmonary
arterial pressure arising from a heterogeneous range of diseases that has a deteriorating …

Clinical phenotype and outcomes of pulmonary hypertension associated with myeloproliferative neoplasms: a population-based study

D Montani, P Thoré, X Mignard, X Jaïs… - American Journal of …, 2023 - atsjournals.org
Rationale: Precapillary pulmonary hypertension (PH) is a rare and largely unrecognized
complication of myeloproliferative neoplasms (MPNs), including polycythemia vera (PV) …

Long-term outcome of children with newly diagnosed pulmonary arterial hypertension: results from the global TOPP registry

MJ Ploegstra, DD Ivy, M Beghetti… - … Journal-Quality of …, 2024 - academic.oup.com
Abstract Background and aims The Tracking Outcomes and Practice in Pediatric Pulmonary
Hypertension (TOPP) registry is a global network established to gain insights into the …

Tricuspid regurgitation: right ventricular volume versus pressure load

R Naeije, K Tello, M D'Alto - Current Heart Failure Reports, 2023 - Springer
Abstract Purpose of the Review Tricuspid regurgitation is associated with increased mortality
in proportion to right ventricular adaptation to increased volume loading and pulmonary …

Time to diagnosis of pulmonary hypertension and diagnostic burden: A retrospective analysis of nationwide US healthcare data

EM Didden, E Lee, J Wyckmans, D Quinn… - Pulmonary …, 2023 - Wiley Online Library
The main aim of this analysis was to investigate time from symptom onset (chronic
unexplained dyspnoea [CUD]) to diagnosis of Group 1 pulmonary hypertension (PH) …

GLI1+ Cells Contribute to Vascular Remodeling in Pulmonary Hypertension

X Chu, V Kheirollahi, A Lingampally… - Circulation …, 2024 - Am Heart Assoc
BACKGROUND: The precise origin of newly formed ACTA2+ (alpha smooth muscle actin-
positive) cells appearing in nonmuscularized vessels in the context of pulmonary …

Acquired disorders of mitochondrial metabolism and dynamics in pulmonary arterial hypertension

NM Breault, D Wu, A Dasgupta, KH Chen… - Frontiers in Cell and …, 2023 - frontiersin.org
Pulmonary arterial hypertension (PAH) is an orphan disease of the cardiopulmonary unit
that reflects an obstructive pulmonary vasculopathy and presents with hypertrophy …

Myeloid-derived suppressor cells and pulmonary hypertension

H Zhang, QW Li, YY Li, X Tang, L Gu… - Frontiers in …, 2023 - frontiersin.org
Pulmonary hypertension (PH) is a chronic pulmonary vascular disorder characterized by an
increase in pulmonary vascular resistance and pulmonary arterial pressure. The detailed …

[HTML][HTML] New therapeutic approach for tricuspid regurgitation: transcatheter tricuspid valve replacement or repair

DI Blusztein, RT Hahn - Frontiers in Cardiovascular Medicine, 2023 - frontiersin.org
The tricuspid valve is a complex structure with normal function dependent on the leaflet
morphology, right atrial and annular dynamics, and right ventricular and chordal support …