ABSTRACT Introduction: Intravenous Immunoglobulin preparations have long been used as
an effective therapeutic approach to patients with predominant antibody deficiencies. The …

Background: Primary immunodeficiency diseases (PIDs) refers to genetic conditions that are
typically distinguished by weakened host defense and a higher susceptibility to infection …

Background: Inborn Errors of Immunity (IEI) include a vast array of immunity disorders that
are diagnosed early in life and that are associated with a high disease burden. Studies on …

Background Primary immunodeficiencies are a heterogeneous group of genetic diseases
caused by one or more abnormalities in the immune system. Although pulmonary …

Primary immunodeficiencies (PID) are a heterogeneous group of inherited disorders, the
etiology are the defects in the development or function of the immune system. The principal …

El nivel de conocimiento sobre las Inmunodeficiencias Primarias (IP) en el médico de primer
contacto incide en la morbimortalidad de este grupo de enfermedades. En ese contexto, el …

Background: Primary immunodeficiencies (PIDs) are inherited disorders in which one or
several components of the immune system are defective. Immunoglobulin replacement …

Objetivo: Describir las características clínicas, laboratoriales y terapéuticas de niños y
adolescentes con inmunodeficiencia primaria. Metodología: Estudio observacional …

Аннотация Первичные иммунодефициты (ПИД) обусловлены дефектами в генах,
контролирующих работу иммунной системы. Мутации могут возникать de novo или …

Primer immün yetmezlik bozuklukları (PİYB), bağışıklık sistemindeki bir veya daha fazla
anormalliğin neden olduğu heterojen bir genetik hastalık grubudur. B hücresi ve antikor …