Influence of hormonal functional status on survival in adrenocortical carcinoma: systematic review and meta-analysis

T Vanbrabant, M Fassnacht, G Assie… - European journal of …, 2018 - academic.oup.com
Objective Adrenocortical carcinoma (ACC) is a malignancy with a poor prognosis. Many
publications in ACC report on risk factors for a poor outcome; one risk factor studied is …

Adrenocortical carcinomas and malignant phaeochromocytomas: ESMO–EURACAN Clinical Practice Guidelines for diagnosis, treatment and follow-up

M Fassnacht, G Assie, E Baudin… - Annals of …, 2020 - annalsofoncology.org
Two different primary malignancies can arise from the adrenal gland: adrenocortical
carcinoma (ACC) from the adrenal cortex and malignant phaeochromocytoma from the …

New perspectives for mitotane treatment of adrenocortical carcinoma

S Puglisi, A Calabrese, V Basile, A Pia… - Best practice & research …, 2020 - Elsevier
Adrenocortical carcinoma (ACC) is an aggressive cancer characterized by poor survival.
Apart from radical surgery, there is a limited range of therapeutic options and mitotane …

European Society of Endocrinology Clinical Practice Guidelines on the management of adrenocortical carcinoma in adults, in collaboration with the European Network …

M Fassnacht, OM Dekkers, T Else… - European journal of …, 2018 - academic.oup.com
Adrenocortical carcinoma (ACC) is a rare and in most cases steroid hormone-producing
tumor with variable prognosis. The purpose of these guidelines is to provide clinicians with …

Long-term outcomes of adjuvant mitotane therapy in patients with radically resected adrenocortical carcinoma

A Berruti, S Grisanti, A Pulzer, M Claps… - The Journal of …, 2017 - academic.oup.com
Context: In 2007, a retrospective case-control study provided evidence that adjuvant
mitotane prolongs recurrence-free survival (RFS) in patients with radically resected …

Adjuvant mitotane versus surveillance in low-grade, localised adrenocortical carcinoma (ADIUVO): an international, multicentre, open-label, randomised, phase 3 trial …

M Terzolo, M Fassnacht, P Perotti, R Libé… - The Lancet Diabetes & …, 2023 - thelancet.com
Background Adjuvant treatment with mitotane is commonly used after resection of
adrenocortical carcinoma; however, treatment remains controversial, particularly if risk of …

S-GRAS score for prognostic classification of adrenocortical carcinoma: an international, multicenter ENSAT study

YS Elhassan, B Altieri, S Berhane… - European Journal of …, 2022 - academic.oup.com
Objective Adrenocortical carcinoma (ACC) has an aggressive but variable clinical course.
Prognostic stratification based on the European Network for the Study of Adrenal Tumours …

Adrenocortical carcinoma: current state of the art, ongoing controversies, and future directions in diagnosis and treatment

OA Shariq, TJ McKenzie - Therapeutic Advances in Chronic …, 2021 - journals.sagepub.com
Adrenocortical carcinoma (ACC) is a rare, aggressive malignancy with an annual incidence
of~ 1 case per million population. Differentiating between ACC and benign adrenocortical …

American Association of Clinical Endocrinology Disease state clinical review on the evaluation and management of adrenocortical carcinoma in an adult: a practical …

K Kiseljak-Vassiliades, I Bancos, A Hamrahian… - Endocrine Practice, 2020 - Elsevier
Objective: The aim of this Disease State Clinical Review is to provide a practical approach to
patients with newly diagnosed adrenocortical carcinoma, as well as to follow-up and …

Management of adrenocortical carcinoma: are we making progress?

B Kiesewetter, P Riss, C Scheuba… - Therapeutic …, 2021 - journals.sagepub.com
Adrenocortical carcinoma (ACC) is a rare malignancy characterized by aggressive biology
and potential endocrine activity. Surgery can offer cure for localized disease but more than …