Cystic fibrosis foundation pulmonary guidelines. Use of cystic fibrosis transmembrane conductance regulator modulator therapy in patients with cystic fibrosis

CL Ren, RL Morgan, C Oermann… - Annals of the …, 2018 - atsjournals.org
Rationale: Cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators
are a new class of medications targeting the underlying defect in CF. Ivacaftor (IVA) and IVA …

Importance of off-label options for treating serious lung diseases

BP O'Sullivan - Annals of the American Thoracic Society, 2016 - atsjournals.org
The perspective article in this month's issue of AnnalsATS by VanDevanter and colleagues
(pp. 1890–1893) raises broad questions about the use of federally approved drugs for …