[HTML][HTML] Evans' syndrome: from diagnosis to treatment

S Audia, N Grienay, M Mounier, M Michel… - Journal of clinical …, 2020 - mdpi.com
Evans' syndrome (ES) is defined as the concomitant or sequential association of warm auto-
immune haemolytic anaemia (AIHA) with immune thrombocytopenia (ITP), and less …

[HTML][HTML] Primary immunodeficiency

C McCusker, J Upton, R Warrington - Allergy, Asthma & Clinical …, 2018 - Springer
Primary immunodeficiency disorder (PID) refers to a large heterogeneous group of disorders
that result from defects in immune system development and/or function. PIDs are broadly …

Sirolimus is effective in relapsed/refractory autoimmune cytopenias: results of a prospective multi-institutional trial

KL Bride, T Vincent, K Smith-Whitley… - Blood, The Journal …, 2016 - ashpublications.org
Patients with autoimmune multilineage cytopenias are often refractory to standard therapies
requiring chronic immunosuppression with medications with limited efficacy and high …

Evans syndrome: clinical perspectives, biological insights and treatment modalities

JC Jaime-Pérez, PE Aguilar-Calderón… - Journal of blood …, 2018 - Taylor & Francis
Evans syndrome (ES) is a rare and chronic autoimmune disease characterized by
autoimmune hemolytic anemia and immune thrombocytopenic purpura with a positive direct …

Warm antibody autoimmune hemolytic anemia

TA Kalfa - Hematology 2014, the American Society of …, 2016 - ashpublications.org
Autoimmune hemolytic anemia (AIHA) is a rare and heterogeneous disease that affects 1 to
3/100 000 patients per year. AIHA caused by warm autoantibodies (w-AIHA), ie, antibodies …

Intrinsic and extrinsic causes of malignancies in patients with primary immunodeficiency disorders

F Hauck, R Voss, C Urban, MG Seidel - Journal of Allergy and Clinical …, 2018 - Elsevier
Malignancies occur with a higher incidence rate and manifest earlier in life in patients with
primary immunodeficiency disorders (PIDs) than in the general population. However, no …

The United Kingdom primary immune deficiency (UKPID) registry 2012 to 2017

B Shillitoe, C Bangs, D Guzman… - Clinical & …, 2018 - academic.oup.com
This is the second report of the United Kingdom Primary Immunodeficiency (UKPID) registry.
The registry will be a decade old in 2018 and, as of August 2017, had recruited 4758 …

[HTML][HTML] Autoimmune lymphoproliferative syndrome: more than a FAScinating disease

K Bride, D Teachey - F1000Research, 2017 - ncbi.nlm.nih.gov
Autoimmune lymphoproliferative syndrome (ALPS) is an inherited syndrome characterized
by abnormal lymphocyte survival caused by failure of apoptotic mechanisms to maintain …

How I manage Evans syndrome and AIHA cases in children

M Miano - British journal of haematology, 2016 - Wiley Online Library
Summary The management of Evans Syndrome in children is challenging due to the lack of
evidence‐based data on treatment. Steroids, the first‐choice therapy, are successful in …

[HTML][HTML] ALPS, FAS, and beyond: from inborn errors of immunity to acquired immunodeficiencies

F Consonni, E Gambineri, C Favre - Annals of Hematology, 2022 - Springer
Autoimmune lymphoproliferative syndrome (ALPS) is a primary immune regulatory disorder
characterized by benign or malignant lymphoproliferation and autoimmunity. Classically …