The expanding clinical spectrum of extracardiovascular and cardiovascular manifestations of heritable thoracic aortic aneurysm and dissection
TJ Bradley, SC Bowdin, CFJ Morel… - Canadian Journal of …, 2016 - Elsevier
More than 30 heritable conditions are associated with thoracic aortic aneurysm and
dissection (TAAD). Heritable syndromic conditions, such as Marfan syndrome, Loeys-Dietz …
dissection (TAAD). Heritable syndromic conditions, such as Marfan syndrome, Loeys-Dietz …
Aortic events in a nationwide Marfan syndrome cohort
KA Groth, K Stochholm, H Hove, K Kyhl… - Clinical Research in …, 2017 - Springer
Background Marfan syndrome is associated with morbidity and mortality due to aortic
dilatation and dissection. Preventive aortic root replacement has been the standard …
dilatation and dissection. Preventive aortic root replacement has been the standard …
Outcomes of valve-sparing surgery in heritable aortic disorders: results from the AVIATOR registry
V Chauvette, J Kluin, L de Kerchove… - European journal of …, 2022 - academic.oup.com
OBJECTIVES Root reimplantation has been the favoured approach for patients with
heritable aortic disorder requiring valve-sparring root replacement. In the past few years …
heritable aortic disorder requiring valve-sparring root replacement. In the past few years …
[HTML][HTML] Aortic root replacement with bicuspid valve reimplantation: are outcomes and valve durability comparable to those of tricuspid valve reimplantation?
SA Mokashi, BF Rosinski, MY Desai, BP Griffin… - The Journal of Thoracic …, 2022 - Elsevier
Objectives To assess intermediate-term outcomes of aortic root replacement with valve-
sparing reimplantation of bicuspid aortic valves (BAV), compared with tricuspid aortic valves …
sparing reimplantation of bicuspid aortic valves (BAV), compared with tricuspid aortic valves …
Pathophysiology and management of cardiovascular manifestations in Marfan and Loeys–Dietz syndromes
N Takeda, H Yagi, H Hara, T Fujiwara… - International heart …, 2016 - jstage.jst.go.jp
Marfan syndrome (MFS) is an autosomal dominant heritable disorder of connective tissue
that affects the cardiovascular, skeletal, ocular, pulmonary, and nervous systems and is …
that affects the cardiovascular, skeletal, ocular, pulmonary, and nervous systems and is …
Cardiovascular events after aortic root repair in patients with Marfan syndrome
TE David, J Park, M Tatangelo, CP Steve Fan… - Journal of the American …, 2023 - jacc.org
Background The usefulness of aortic valve sparing operations to treat aortic root aneurysm
in patients with Marfan syndrome (MS) remains controversial. Objectives The purpose of this …
in patients with Marfan syndrome (MS) remains controversial. Objectives The purpose of this …
Midterm outcomes of aortic root surgery in patients with Marfan syndrome: a prospective, multicenter, comparative study
JS Coselli, IV Volguina, SA LeMaire… - The Journal of Thoracic …, 2023 - Elsevier
Objective The objective of this study was to compare midterm outcomes of aortic valve-
replacing root replacement (AVR) and aortic valve-sparing root replacement (AVS) …
replacing root replacement (AVR) and aortic valve-sparing root replacement (AVS) …
Recent progress in understanding the natural and clinical histories of the Marfan syndrome
RE Pyeritz - Trends in Cardiovascular Medicine, 2016 - Elsevier
Over the past 4 decades, remarkable progress in understanding the cause, pathogenesis,
and management of the MFS has led to an increase in life expectancy to near normal for …
and management of the MFS has led to an increase in life expectancy to near normal for …
External aortic root support to prevent aortic dilatation in patients with Marfan syndrome
C Izgi, S Newsome, F Alpendurada, E Nyktari… - Journal of the American …, 2018 - jacc.org
Background: Personalized external aortic root support (PEARS) was introduced in 2004 for
prevention of aortic root dilatation in Marfan patients. The individual's aortic root is replicated …
prevention of aortic root dilatation in Marfan patients. The individual's aortic root is replicated …
Improved outcomes of reimplantation vs remodeling in Marfan syndrome: a propensity-matched study
M Elbatarny, TE David, CM David, JCY Chung… - The Annals of Thoracic …, 2023 - Elsevier
Background Valve-sparing root replacement (VSRR) has excellent outcomes when
performed in experienced centers in well-selected patients. It is suggested that …
performed in experienced centers in well-selected patients. It is suggested that …