Electrical storm is a medical emergency characterized by ventricular arrythmia recurrence
that can lead to hemodynamic instability. The incidence of this clinical condition is rising …

Background Unfortunately, some patients with long QT syndrome (LQTS) experience
breakthrough cardiac events (BCEs) despite maximal therapy. Small studies have shown …

Background The potential benefit of implantable cardioverter-defibrillator (ICD) therapy in
individuals with inherited arrhythmia syndromes is well known. However, it is not deprived of …

Medications such as ß-blockers are currently the primary treatment for patients with
hereditary arrhythmia syndromes such as long QT syndrome (LQTS) and catecholaminergic …

There is little doubt that congenital long QT syndrome (LQTS) is the best known and best
understood of the channelopathies. Partly, because its first description goes back already 60 …

Background Primary treatment of long QT syndrome (LQTS) currently consists of beta-
blocker therapy, although an implantable cardioverter-defibrillator (ICD) is considered for …

While published guidelines are useful in the care of patients with long-QT syndrome, it can
be difficult to decide how to apply the guidelines to individual patients, particularly those with …

The implantable cardioverter-defibrillator significantly improves survival in patients with
malignant ventricular arrhythmias but does not target the underlying pathological substrate …

Long QT syndrome (LQTS) is an inherited (autosomal dominant) channelopathy associated
with susceptibility to ventricular arrhythmias due to malfunction of ion channels in …