Left ventricular hypertrabeculation (LVHT) or noncompaction is a myocardial abnormality of
unknown aetiology, frequently associated with monogenic disorders, particularly …

Muscular dystrophy (MD) connotes a heterogeneous group of inherited disorders
characterized by progressive wasting and weakness of the skeletal muscles. In several …

Background Left ventricular hypertrabeculation (LVHT), also known as noncompaction or
spongy myocardium, is a cardiac abnormality of unknown etiology and pathogenesis …

Myotonic dystrophy (MD) is a multisystem, autosomal dominant disorder best known for its
skeletal muscle manifestations. Cardiac manifestations arise as a result of myocardial fatty …

Despite advances in detection, comprehensive clinical, pathological, genetic, and family
studies are necessary to define the phenotypic overlap with other cardiomyopathies. Without …

Objectives The heart is frequently affected in neuromuscular disorders (NMDs). Some of
these patients even experience sudden cardiac death (SCD). In the following review, we …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

Cardiac disease is a common clinical manifestation present in a variety of neuromuscular
disorders, most notably the muscular dystrophies. Heart disease may produce the …

Background: Though not obvious at a first glance, myopathies may be associated with
ischemic stroke. Stroke-like episodes resemble ischemic stroke only to some extent but are …

Introduction: When> 3 trabeculations associated with interventricular recesses are found,
this is termed 'left ventricular hypertrabeculation/noncompaction'(LVHT). Cardiac-imaging …