Pediatric cardiomyopathies

TM Lee, DT Hsu, P Kantor, JA Towbin… - Circulation …, 2017 - Am Heart Assoc
Pediatric cardiomyopathies are rare diseases with an annual incidence of 1.1 to 1.5 per 100
000. Dilated and hypertrophic cardiomyopathies are the most common; restrictive …

Cardiomyopathies: an overview

E Braunwald - Circulation research, 2017 - Am Heart Assoc
The nonischemic cardiomyopathies are a diverse group of cardiac disorders that frequently
cause heart failure and death and are now recognized with increasing frequency. There has …

The 2016 International Society for Heart Lung Transplantation listing criteria for heart transplantation: a 10-year update

MR Mehra, CE Canter, MM Hannan… - The Journal of Heart …, 2016 - jhltonline.org
In 2005, the International Society for Heart and Lung Transplantation (ISHLT) Board of
Directors commissioned the development of the first International Listing Criteria for Heart …

[PDF][PDF] RASopathy-associated cardiomyopathy

A Albakri - Int Med Care, 2019 - m.script-one.com
RASopathies are a family of developmental disorders that share germline mutations in the
components of the RAS-MAPK pathway leading to dysregulated signalling. A high …

Systematic literature review on the incidence and prevalence of heart failure in children and adolescents

RE Shaddy, AT George, T Jaecklin, EN Lochlainn… - Pediatric …, 2018 - Springer
While the epidemiology of adult heart failure has been extensively researched, this
systematic review addresses the less well characterized incidence and prevalence of …

[HTML][HTML] Importance of genetic evaluation and testing in pediatric cardiomyopathy

M Tariq, SM Ware - World journal of cardiology, 2014 - ncbi.nlm.nih.gov
Pediatric cardiomyopathies are clinically heterogeneous heart muscle disorders that are
responsible for significant morbidity and mortality. Phenotypes include hypertrophic …

Impact of mode of failure and end-organ dysfunction on the survival of adult Fontan patients undergoing cardiac transplantation

B Murtuza, A Hermuzi, DS Crossland… - European journal of …, 2017 - academic.oup.com
OBJECTIVES Adults with failing Fontan circulation (FFC) represent a heterogeneous, high-
risk group for cardiac transplantation with poor reported outcomes. We studied the impact of …

Focus on Paediatric Restrictive Cardiomyopathy: Frequently Asked Questions

M Zampieri, C Di Filippo, C Zocchi, V Fico, C Golinelli… - Diagnostics, 2023 - mdpi.com
Restrictive cardiomyopathy (RCM) is characterized by restrictive ventricular pathophysiology
determined by increased myocardial stiffness. While suspicion of RCM is initially raised by …

'End-stage'heart failure therapy: potential lessons from congenital heart disease: from pulmonary artery banding and interatrial communication to parallel circulation

D Schranz, H Akintuerk, NF Voelkel - Heart, 2017 - heart.bmj.com
The final therapy of 'end-stage heart failure'is orthotopic heart, lung or heart-lung
transplantation. However, these options are not available for many patients worldwide …

[HTML][HTML] Outcomes and risk factors for heart transplantation in children with congenital heart disease

B Alsoufi, S Deshpande, C McCracken, B Kogon… - The Journal of Thoracic …, 2015 - Elsevier
Objective Heart transplantation in children with underlying congenital heart disease has
traditionally been associated with inferior outcomes. We report our single institution …