Ventricular non-compaction review

S Srivastava, M Yavari, A Al-Abcha, S Banga… - Heart Failure …, 2022 - Springer
Left ventricular non-compaction cardiomyopathy (LVNC) is a rare and unclassified
cardiomyopathy that carries the potential to cause heart failure, arrhythmias, and embolic …

[HTML][HTML] Left ventricular noncompaction—a systematic review of risk factors in the pediatric population

K Łuczak-Woźniak, B Werner - Journal of Clinical Medicine, 2021 - mdpi.com
Left ventricular noncompaction (LVNC) is a heterogeneous, often hereditary group of
diseases, which may have diverse clinical manifestations. This article reviews the risk factors …

LncRNA-Smad7 mediates cross-talk between Nodal/TGF-β and BMP signaling to regulate cell fate determination of pluripotent and multipotent cells

X Kong, K Yan, P Deng, H Fu, H Sun… - Nucleic Acids …, 2022 - academic.oup.com
Transforming growth factor β (TGF-β) superfamily proteins are potent regulators of cellular
development and differentiation. Nodal/Activin/TGF-β and BMP ligands are both present in …

[HTML][HTML] Endothelial-myocardial angiocrine signaling in heart development

H Kim, M Wang, DT Paik - Frontiers in Cell and Developmental …, 2021 - frontiersin.org
Vascular endothelial cells are a multifunctional cell type with organotypic specificity in their
function and structure. In this review, we discuss various subpopulations of endothelial cells …

[HTML][HTML] Left ventricular noncompaction is associated with valvular regurgitation and a variety of arrhythmias

Q Li, L Miao, L Xia, HY Abdelnasser, F Zhang… - Journal of …, 2022 - mdpi.com
Left ventricular noncompaction (LVNC) is a type of cardiomyopathy characterized
anatomically by prominent ventricular trabeculation and deep intertrabecular recesses. The …

[HTML][HTML] Left ventricular noncompaction—a rare cause of triad: heart failure, ventricular arrhythmias, and systemic embolic events: a case report

D Toader, A Paraschiv, P Tudorașcu… - Journal of Medical Case …, 2021 - Springer
Background Left ventricular noncompaction is a rare cardiomyopathy characterized by a
thin, compacted epicardial layer and a noncompacted endocardial layer, with trabeculations …

[HTML][HTML] The Rare Condition of Left Ventricular Non-Compaction and Reverse Remodeling

C Bustea, AF Bungau, DM Tit, DC Iovanovici, MM Toma… - Life, 2023 - mdpi.com
Left ventricular non-compaction (LVNC) is a rare disease defined by morphological criteria,
consisting of a two-layered ventricular wall, a thin compacted epicardial layer, and a thick …

[HTML][HTML] Myocardial edema: a rare but specific manifestation of neonatal capillary leak syndrome

J Liu, YQ Gao - Diagnostics, 2023 - mdpi.com
Capillary leak syndrome (CLS) is a rare, potentially life-threatening systemic disease with a
mortality rate of more than 30%. Its major clinical manifestation and diagnostic basis are …

[HTML][HTML] Multimodality Imaging and Biomarker Approach to Characterize the Pathophysiology of Heart Failure in Left Ventricular Non-Compaction with Preserved …

IS Visoiu, RC Rimbas, AI Nicula… - Journal of Clinical …, 2023 - mdpi.com
Left ventricular non-compaction (LVNC) with preserved ejection fraction (EF) is still a
controverted entity. We aimed to characterize structural and functional changes in LVNC …

Biallelic PKP2 loss of function variants are associated with a lethal perinatal-onset biventricular dilated cardiomyopathy with excessive trabeculations and ventricular …

J Gibb, E Wall, E Fields, A Seale… - Journal of Medical …, 2024 - jmg.bmj.com
Homozygous plakophilin-2 (PKP2) variants have been identified as a cause of a lethal form
of dilated cardiomyopathy with excessive trabeculations (DCM-ET) in three cases. We report …