Contemporary Approach to Neurofibromatosis Type 1–Associated Malignant Peripheral Nerve Sheath Tumors

AC Hirbe, CA Dehner, E Dombi, V Eulo… - American Society of …, 2024 - ascopubs.org
Most malignant peripheral nerve sheath tumors (MPNSTs) are clinically aggressive high-
grade sarcomas, arising in individuals with neurofibromatosis type 1 (NF1) at a significantly …