The changing epidemiology of cystic fibrosis: the implications for adult care

PR Burgel, E Burnet, L Regard, C Martin - Chest, 2023 - Elsevier
Cystic fibrosis (CF) is a genetic disease in which mutations in the gene encoding for the CF
transmembrane conductance regulator protein result in a multisystem disease dominated by …

The impact of pancreatic exocrine diseases on the β-cell and glucose metabolism—a review with currently available evidence

M Ciochina, DV Balaban, G Manucu, M Jinga… - Biomolecules, 2022 - mdpi.com
Pancreatic exocrine and endocrine dysfunctions often come together in the course of
pancreatic diseases as interdependent manifestations of the same organ. However, the …

ESPEN-ESPGHAN-ECFS guideline on nutrition care for cystic fibrosis

M Wilschanski, A Munck, E Carrion, M Cipolli, S Collins… - Clinical Nutrition, 2024 - Elsevier
Background Nutritional status is paramount in Cystic Fibrosis (CF) and is directly correlated
with morbidity and mortality. The first ESPEN-ESPGHAN-ECFS guidelines on nutrition care …

Cystic fibrosis and fat malabsorption: Pathophysiology of the cystic fibrosis gastrointestinal tract and the impact of highly effective CFTR modulator therapy

CM McDonald, EK Reid, JF Pohl… - Nutrition in Clinical …, 2024 - Wiley Online Library
Cystic fibrosis (CF) is a progressive, genetic, multi‐organ disease affecting the respiratory,
digestive, endocrine, and reproductive systems. CF can affect any aspect of the …

Improvement of lipid and lipoprotein profiles in children and adolescents with cystic fibrosis on CFTR modulator therapy

T Yuzyuk, CM McDonald, LM Zuromski, I De Biase… - Journal of Cystic …, 2023 - Elsevier
Background Association of a high-fat diet with increased risks of cardiovascular disease
(CVD) and type 2 diabetes, has prompted evaluation of lipids in people with CF (pwCF) …

Low vitamin K status in adults with cystic fibrosis is associated with reduced body mass index, insulin secretion, and increased pseudomonal colonization

C Bergeron, KJ Potter, V Boudreau… - Applied Physiology …, 2023 - cdnsciencepub.com
Patients with cystic fibrosis (CF) are at high risk of fat-soluble vitamin deficiencies, even with
supplementation. The contribution of a suboptimal vitamin K status to respiratory and …

Marginal association of fasting blood glucose with the risk of cystic fibrosis-related diabetes

KJ Potter, A Bonhoure, V Boudreau, F Tremblay… - Annales d' …, 2023 - Elsevier
Objectives Cystic fibrosis-related diabetes (CFRD) may be diagnosed by fasting blood
glucose≥ 7.0 mmol/L and/or glucose≥ 11.1 mmol/L following oral glucose tolerance test …

[HTML][HTML] MicroRNA global profiling in cystic fibrosis cell lines reveals dysregulated pathways related with inflammation, cancer, growth, glucose and lipid metabolism …

C Catellani, F Cirillo, S Graziano… - Acta Bio Medica …, 2022 - ncbi.nlm.nih.gov
Methods: We assessed the changes in miRNAs and subsequently identified the affected
molecular pathways using CFBE41o-, and IB3 human immortalized cell lines since they …

Caractérisation du statut en vitamine K chez les patients adultes atteints de la fibrose kystique

C Bergeron - 2022 - papyrus.bib.umontreal.ca
Les déficiences en vitamines liposolubles sont fréquentes chez les patients atteints de la
fibrose kystique (FK), mais la fréquence et les implications cliniques d'un déficit en vitamine …

Šećerna bolest pridružena cističnoj fibrozi

H Jelavić - 2021 - repozitorij.unizg.hr
Sažetak Cistična fibroza (CF) je najčešća autosomno-recesivno nasljedna bolest u ljudi
bijele rase koja bitno skraćuje životni vijek. Posljednjih smo desetljeća došli do brojnih novih …