Mortality and survival in idiopathic pulmonary fibrosis: a systematic review and meta-analysis

Q Zheng, IA Cox, JA Campbell, Q Xia… - ERJ open …, 2022 - Eur Respiratory Soc
Background There are substantial advances in diagnosis and treatment for idiopathic
pulmonary fibrosis (IPF), but without much evidence available on recent mortality and …

Metabolic dysregulation in idiopathic pulmonary fibrosis

E Bargagli, RM Refini, M d'Alessandro… - International journal of …, 2020 - mdpi.com
Idiopathic pulmonary fibrosis (IPF) is a fibroproliferative disorder limited to the lung. New
findings, starting from our proteomics studies on IPF, suggest that systemic involvement with …

Long-term follow-up of patients with idiopathic pulmonary fibrosis treated with pirfenidone or nintedanib: a real-life comparison study

P Cameli, RM Refini, L Bergantini… - Frontiers in Molecular …, 2020 - frontiersin.org
Background Pirfenidone and nintedanib are the sole pharmacological therapies currently
approved for idiopathic pulmonary fibrosis (IPF). Limited comparison data is available in …

Serum concentrations of KL-6 in patients with IPF and lung cancer and serial measurements of KL-6 in IPF patients treated with antifibrotic therapy

M d'Alessandro, L Bergantini, P Cameli, M Pieroni… - Cancers, 2021 - mdpi.com
Simple Summary Evaluation of the prognostic significance of serial measurements of serum
concentrations of Krebs von den Lungen-6 (KL-6) showed that an annual increment in KL-6 …

Understanding idiopathic pulmonary fibrosis-clinical features, molecular mechanism and therapies

GS Suri, G Kaur, CK Jha, M Tiwari - Experimental gerontology, 2021 - Elsevier
Idiopathic pulmonary fibrosis (IPF) is a chronic lung fibrosing disease with high prevalence
that has a prognosis worse than many cancers. There has been a recent influx of new …

Markers of bronchiolitis obliterans syndrome after lung transplant: between old knowledge and future perspective

D Cavallaro, M Guerrieri, S Cattelan, G Fabbri, S Croce… - Biomedicines, 2022 - mdpi.com
Bronchiolitis obliterans syndrome (BOS) is the most common form of CLAD and is
characterized by airflow limitation and an obstructive spirometric pattern without high …

Extracellular vesicle surface signatures in IPF patients: A multiplex bead-based flow cytometry approach

M d'Alessandro, P Soccio, L Bergantini, P Cameli… - Cells, 2021 - mdpi.com
Background: Extracellular vesicles (EVs) are secreted by cells from their membrane within
circulation and body fluids. Knowledge of the involvement of EVs in pathogenesis of lung …

Assessing the effectiveness of pirfenidone in idiopathic pulmonary fibrosis: long-term, real-world data from European IPF Registry (eurIPFreg)

E Krauss, S Tello, J Wilhelm, J Schmidt… - Journal of clinical …, 2020 - mdpi.com
Background: Idiopathic pulmonary fibrosis (IPF) is a chronic progressive fibrotic pulmonary
disease with rising incidence. In this study the effectiveness of pirfenidone, as measured by …

Integrated approach to bronchoalveolar lavage cytology to distinguish interstitial lung diseases

L Bergantini, M d'Alessandro, P Cameli… - European Journal of …, 2021 - Elsevier
Background Broncho-alveolar lavage (BAL) is a safe diagnostic procedure, useful for
differentiating fibrotic lung disorders and for excluding malignancy and infection. A recent …

Combined sarcoidosis and idiopathic pulmonary fibrosis (CSIPF): a new phenotype or a fortuitous overlap? Scoping review and case series

L Bergantini, G Nardelli, M d'Alessandro… - Journal of Clinical …, 2022 - mdpi.com
Idiopathic pulmonary fibrosis (IPF) and sarcoidosis are two distinct clinical entities with
different aetiology, epidemiology, risk factors, symptoms and chest imaging. A number of …