Einleitung: Die orale CFTR (cystic fibrosis transmembrane conductance regulator)-
Modulator-Kombinationstherapie Ivacaftor/Tezacaftor/Elexacaftor (IVA/TEZ/ELX) hat die …

RESUMO O objetivo deste trabalho é avaliar a capacidade de exercício e nível de atividade
física diária de crianças e adolescentes com fibrose cística e associar com estado …

The article presents a review for studies and research conducted on interstitial lung disease,
pulmonary vascular disease, pulmonary function, paediatric lung disease, cystic fibrosis and …

Physical activity defined as any bodily muscular movement, which results in energy
expenditure above resting baseline values, is an integral component to health and well …

Cystic fibrosis (CF) is a life-shortening genetic disease, affecting multiple life domains
including physical activity (PA). Although higher PA levels are associated with multiple …

To be included potential participants had to have access to the internet via a computer or
mobile device, and they (or their carer) able to provide written informed consent. Potential …

Cystic fibrosis (CF) is a rare, autosomal recessive multiorgan genetic disease. Peripheral
muscle weakness and reduced lung function are prevalent in individuals with CF. Handgrip …

Background Physical activity (PA) is a well-established therapeutic modality for the
maintenance and improvement of long-term health in cystic fibrosis (CF). Healthcare …

Maintaining adequate levels of physical activity (PA) is important for the health and well-
being of children and young people with cystic fibrosis (CYPwCF). Identifying who maintains …

Abstract INTRODUCTION: Cystic Fibrosis (CF) is an autosomal recessive disorder due to
mutations in the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene …