Background A high-fat, high-calorie diet is recommended in patients with cystic fibrosis (CF)
as it improves nutritional status, respiratory health and longevity. In the general population …

Purpose: Exercise intolerance, evaluated by O 2 consumption, predicts mortality in Cystic
Fibrosis (CF). People with CF exhibit skeletal muscle dysfunctions that may contribute to an …

Caring for people with cystic fibrosis has changed considerably since the first description of
the disorder and continues to evolve in the era of highly effective modulator therapy. These …

Le développement des modulateurs du cystic fibrosis conductance transmembrane
regulator (CFTR) pour les patients atteints de mucoviscidose (MV) et éligibles à ces …

Vitamin D is an essential hydrophobic micronutrient. There are at least seven different forms
of vitamin D, however, only D2 and D3 are considered to be its biologically active forms in …

Background Patients with cystic fibrosis (CF) have a reduced intestinal absorption of
cholesterol and in a preliminary study we observed differences in plasma sterol profile …

Cystic fibrosis (CF) patients are insulin-resistant with regards to suppression of hepatic
glucose production and proteolysis, but the effect of insulin on adipose free fatty acid (FFA) …

Background Cystic fibrosis lung disease is characterized by chronic bacterial infections in
the setting of mucus abnormalities. Patients experience periodic exacerbations that manifest …

Proteins involved in lipoprotein metabolism can modulate cardiovascular health. While often
measured to assess adult metabolic diseases, little is known about the proteomes of …

OBJETIVO: Revisar e discutir evidências sobre a avaliação do estado nutricional e as
recomendações para o tratamento nutricional de crianças e adolescentes com fibrose …