Two antifibrotic medications (nintedanib and pirfenidone) were recommended
(conditionally) for the treatment of patients with idiopathic pulmonary fibrosis (IPF) in the …

Fibrosis, the progressive accumulation of connective tissue that occurs in response to injury,
causes irreparable organ damage and may result in organ failure. The few available …

Objective To determine the prognostic value of pulmonary function test (PFT) trends at 1 and
2 years in interstitial lung disease (ILD) associated with systemic sclerosis (SSc). Methods …

Rationale: Respiratory-related hospitalizations of patients with idiopathic pulmonary fibrosis
(IPF) are more frequent than those for acute IPF exacerbations and are associated with poor …

Importance Alteration in lung microbes is associated with disease progression in idiopathic
pulmonary fibrosis. Objective To assess the effect of antimicrobial therapy on clinical …

Pulmonary fibrosis (PF) is a progressive, and life-threatening interstitial lung disease which
causes scarring in the lung parenchyma and thereby affects architecture and functioning of …

Idiopathic pulmonary fibrosis (IPF) is a chronic, debilitating, fibrotic lung disease leading to
respiratory failure and ultimately to death. Being the prototype of interstitial lung diseases …

Rationale: Mortality prediction is well studied in idiopathic pulmonary fibrosis (IPF), but little
is known about predictors of premortality disease progression. Identification of patients at …

The objective of this study was to investigate the reliability, feasibility and analytical impact of
home-based measurement of forced vital capacity (FVC) and dyspnoea as clinical endpoints …

Idiopathic pulmonary fibrosis (IPF), the most common form of fibrosing idiopathic interstitial
pneumonia, is an inexorably progressive disease with a 5-year survival of~ 20%. In the last …