The many forms of vasculitis are characterized by inflammation of blood vessels, leading to
potentially long-term sequelae including vision loss, aneurysm formation and kidney failure …

Immunoglobulin A vasculitis (IgAV), formerly known as Henoch-Schönlein purpura, is the
most common systemic vasculitis in children, characterized by diverse clinical …

Immunoglobin A (IgA) vasculitis (IgAV), formerly called the Henoch-Schönlein purpura
(HSP), is a small vessel vasculitis, characterized by IgA1-dominant immune deposition at …

Abstract Familial Mediterranean fever (FMF)(OMIM# 249100) is the most common hereditary
autoinflammatory disease in the world. FMF is caused by gain of function mutations of MEFV …

(1) Background: Familial Mediterranean Fever (FMF) is the prototypal autoinflammatory
disease, characterized by recurrent bursts of neutrophilic inflammation.(2) Methods: In this …

Familial Mediterranean fever (FMF) is the most common monogenic autoinflammatory
disease manifesting with phenotypic heterogeneity. The phenotype–genotype correlation is …

Familial Mediterranean fever (FMF) is a hereditary autoinflammatory disease characterized
by recurrent attacks of fever and polyserositis. Its first description as a new entity was …

We now have recommendations for assessing genetic analysis of the MEFV gene and how
to reliably classify a patient as FMF. We await further data to understand the contributing …

The past 25 years have seen major novel developments in the field of paediatric
rheumatology. The concept of autoinflammation was introduced to this field, and medicine …

Behçet disease (BD) and familial Mediterranean fever (FMF) are two inflammatory disorders
that share many features including historical background, ethnical distribution and …