Cellular functions of the protein kinase ATM and their relevance to human disease

JH Lee, TT Paull - Nature Reviews Molecular Cell Biology, 2021 - nature.com
The protein kinase ataxia telangiectasia mutated (ATM) is a master regulator of double-
strand DNA break (DSB) signalling and stress responses. For three decades, ATM has been …

CRISPR-based functional genomics for neurological disease

M Kampmann - Nature Reviews Neurology, 2020 - nature.com
Neurodegenerative, neurodevelopmental and neuropsychiatric disorders are among the
greatest public health challenges, as many lack disease-modifying treatments. A major …

Generation of functional human 3D cortico-motor assembloids

J Andersen, O Revah, Y Miura, N Thom, ND Amin… - Cell, 2020 - cell.com
Neurons in the cerebral cortex connect through descending pathways to hindbrain and
spinal cord to activate muscle and generate movement. Although components of this …

[HTML][HTML] Neurodegenerative disease: models, mechanisms, and a new hope

AD Gitler, P Dhillon, J Shorter - Disease models & …, 2017 - journals.biologists.com
Neurodegeneration is a feature of many debilitating, incurable diseases that are rapidly
rising in prevalence, such as Parkinson's disease. There is an urgent need to develop new …

ALS-implicated protein TDP-43 sustains levels of STMN2, a mediator of motor neuron growth and repair

JR Klim, LA Williams, F Limone… - Nature …, 2019 - nature.com
The findings that amyotrophic lateral sclerosis (ALS) patients almost universally display
pathological mislocalization of the RNA-binding protein TDP-43 and that mutations in its …

GGGGCC repeat expansion in C9orf72 compromises nucleocytoplasmic transport

BD Freibaum, Y Lu, R Lopez-Gonzalez, NC Kim… - Nature, 2015 - nature.com
Abstract The GGGGCC (G4C2) repeat expansion in a noncoding region of C9orf72 is the
most common cause of sporadic and familial forms of amyotrophic lateral sclerosis and …

[HTML][HTML] Rapid single-step induction of functional neurons from human pluripotent stem cells

Y Zhang, CH Pak, Y Han, H Ahlenius, Z Zhang… - Neuron, 2013 - cell.com
Available methods for differentiating human embryonic stem cells (ESCs) and induced
pluripotent cells (iPSCs) into neurons are often cumbersome, slow, and variable …

Generation and expansion of highly pure motor neuron progenitors from human pluripotent stem cells

ZW Du, H Chen, H Liu, J Lu, K Qian, CTL Huang… - Nature …, 2015 - nature.com
Human pluripotent stem cells (hPSCs) have opened new opportunities for understanding
human development, modelling disease processes and developing new therapeutics …

[HTML][HTML] Pyramidal neurons derived from human pluripotent stem cells integrate efficiently into mouse brain circuits in vivo

I Espuny-Camacho, KA Michelsen, D Gall, D Linaro… - Neuron, 2013 - cell.com
The study of human cortical development has major implications for brain evolution and
diseases but has remained elusive due to paucity of experimental models. Here we found …

Generation of induced neuronal cells by the single reprogramming factor ASCL1

S Chanda, CE Ang, J Davila, CH Pak, M Mall, QY Lee… - Stem cell reports, 2014 - cell.com
Direct conversion of nonneural cells to functional neurons holds great promise for
neurological disease modeling and regenerative medicine. We previously reported rapid …