Excessive trabeculation, often referred to as “noncompacted” myocardium, has been
described at all ages, from the fetus to the adult. Current evidence for myocardial …

Left ventricular noncompaction (LVNC) describes a ventricular wall anatomy characterized
by prominent left ventricular (LV) trabeculae, a thin compacted layer, and deep …

Background—Left ventricular noncompaction (LVNC) is a genetically and phenotypically
heterogeneous disease and, although increasingly recognized in clinical practice, there is a …

Objectives: Review the etiology of left ventricular non-compaction cardiomyopathy. Describe
the evaluation of left ventricular non-compaction cardiomyopathy. Summarize the treatment …

Barth syndrome is characterized in affected males by cardiomyopathy, neutropenia, skeletal
myopathy, prepubertal growth delay, and distinctive facial gestalt (most evident in infancy); …

Duchenne muscular dystrophy (DMD) is a fatal inherited genetic disorder that results in
progressive muscle weakness and ultimately loss of ambulation, respiratory failure and …

Supporting mitochondrial function is one of the therapeutic strategies that improve the
functioning of skeletal muscle in Duchenne muscular dystrophy (DMD). In this work, we …

Background The dystrophinopathies include Duchenne muscular dystrophy (DMD), Becker
muscular dystrophy (BMD), and X‐linked dilated cardiomyopathy (XLDCM). In recent years …

Left ventricular non-compaction (LVNC) is a heterogeneous myocardial disorder
characterized by prominent trabeculae protruding into the left ventricular lumen and deep …

An intricate meshwork of trabeculations lines the luminal side of cardiac ventricles.
Compaction, a developmental process, is thought to reduce trabeculations by adding them …