Rationale: Cystic fibrosis (CF) lung disease starts in early infancy, suggesting that preventive
treatment may be most beneficial. Lung clearance index (LCI) and chest magnetic …

Rationale: Previous cross-sectional studies have demonstrated that chest magnetic
resonance imaging (MRI) is sensitive to detect early lung disease in infants and preschool …

Objectives We hypothesized that non-contrast-enhanced PETRA (pointwise encoding time
reduction with radial acquisition) MR (magnetic resonance) sequencing could be an …

Reproducibility and predictive value on outcome are the main criteria to evaluate the utility of
histological scores. Here we analyze the reproducibility of donor biopsy assessment by …

CFTR modulator therapy with elexacaftor/tezacaftor/ivacaftor (ETI) has been approved for
people with CF and at least one F508del allele in Europe. In the US, the ETI label has been …

Progressive lung disease in cystic fibrosis (CF) is the life-limiting factor of this autosomal
recessive genetic disorder. Increasing implementation of CF newborn screening allows for a …

Rationale: Recent advancements that have been made in magnetic resonance imaging
(MRI) improve our ability to assess pulmonary structure and function in patients with cystic …

Structural and functional defects within the lungs of children with cystic fibrosis (CF) are
detectable soon after birth and progress throughout preschool years often without overt …

Background Dyspnea is common after COVID‐19. Though the underlying mechanisms are
largely unknown, lung perfusion abnormalities could contribute to lingering dyspnea …

Abstract Purpose To validate Fourier decomposition (FD) magnetic resonance (MR) imaging
in cystic fibrosis (CF) patients with dynamic contrast-enhanced (DCE) MR imaging. Materials …