Interventions for promoting participation in shared decision‐making for children and adolescents with cystic fibrosis

H Malone, S Biggar, S Javadpour… - Cochrane Database …, 2019 - cochranelibrary.com
Background Shared decision‐making is important in child and adolescent healthcare
because there is growing international recognition of children and young people's rights to …

Challenges with optimizing nutrition in cystic fibrosis

C Colombo, RM Nobili, G Alicandro - Expert review of respiratory …, 2019 - Taylor & Francis
Introduction. Optimizing nutrition remains the cornerstone of therapy for patients with cystic
fibrosis (CF) since it is associated with better pulmonary function and survival. However, a …

Nutritional status in childhood as a prognostic factor in patients with cystic fibrosis

M Ashkenazi, N Nathan, I Sarouk, BEB Aluma… - Lung, 2019 - Springer
Introduction There is a strong association between cystic fibrosis and malnutrition, mainly
because of the higher energy needs combined with lower intake. There is also a well …

[HTML][HTML] Lack of efficacy of Lactobacillus GG in reducing pulmonary exacerbations and hospital admissions in children with cystic fibrosis: A randomised placebo …

E Bruzzese, V Raia, E Ruberto, R Scotto… - Journal of cystic …, 2018 - Elsevier
Background Intestinal dysbiosis has been described in Cystic Fibrosis (CF) and probiotics
have been proposed to restore microbial composition. Aim of the study was to investigate …

Effects of prolonged proton pump inhibitor treatment on nutritional status and respiratory infection risk in cystic fibrosis: A matched cohort study

L Zazzeron, G Alicandro, V Daccò, C Lanfranchi… - Digestive and Liver …, 2023 - Elsevier
Background Evidence on the effectiveness of proton pump inhibitors (PPI) as adjuvant
therapy to improve maldigestion in people with cystic fibrosis (pwCF) is limited and there is …

[HTML][HTML] The effect of enteral tube feeding in cystic fibrosis: A registry based study

D Libeert, D Declercq, S Wanyama, M Thomas… - Journal of Cystic …, 2018 - Elsevier
Background Long-term effect of enteral tube feeding (ETF) in cystic fibrosis (CF) remains
equivocal. Methods A Belgian CF registry based, retrospective, longitudinal study, evaluated …

Undernutrition is still highly frequent in hospitalized children with cystic fibrosis

L Bouvart, V Raoult, R Hankard, A De Luca… - Archives de …, 2023 - Elsevier
The aim of our study was to assess the nutritional status of hospitalized children with cystic
fibrosis. We extracted data from the ePINUT surveys. Undernutrition was defined as a body …

[HTML][HTML] A survey identifying nutritional needs in a contemporary adult cystic fibrosis cohort

SG Kapnadak, KJ Ramos, AM Lopriore, CH Goss… - BMC nutrition, 2019 - Springer
Background Cystic fibrosis (CF) is a disease in which nutritional barriers are diverse and
common, with malnutrition greatly influencing pulmonary trajectory and overall outcomes …

[HTML][HTML] Nutritional assessment and rehabilitation in children with bronchiectasis and childhood interstitial lung diseases: effects on pulmonary functions and clinical …

A Alsharkawy, E Fouda, A Mujahed… - Egyptian Pediatric …, 2021 - Springer
Background Nutrition is recognized as a modifiable contributor to bronchiectasis and
interstitial lung diseases (ChILD) development and progression. Nutritional interventions …

Liver and pancreatic disease in cystic fibrosis: clinics and drug therapy

C Colombo, G Alicandro, F Corti… - … , Endocrine & Metabolic …, 2016 - ingentaconnect.com
Abnormal functioning of the Cystic Fibrosis (CF) Transmembrane Conductance Regulator
(CFTR) channel impairs mucociliary clearance and promotes chronic bacterial infections in …