BACKGROUND: Aortic stenosis (AS) is encountered in approximately 5% of children with
heart disease. The indications for surgery and the surgical techniques for AS are well …

Objective: Supravalvular aortic stenosis (SVAS) is an uncommon congenital cardiac
anomaly characterized by varying degrees of left ventricular outflow tract obstruction …

OBJECTIVES: Peripheral pulmonary artery stenosis is a rare congenital heart defect
frequently found in association with Williams and Alagille syndromes. Controversy exists …

OBJECTIVES Congenital supravalvular aortic stenosis (SVAS) is a rare form of congenital
outflow tract obstruction and long-term outcomes are scarcely reported. This study aims to …

BACKGROUND: We reviewed our experience with the surgical management of supravalvar
aortic stenosis (SVAS) to determine long-term outcomes and factors related to late …

Williams syndrome (WS) is a relatively rare congenital disorder which manifests across
multiple organ systems with a wide spectrum of severity. Cardiovascular anomalies are the …

Background Supravalvular aortic stenosis (SVAS) represents a heterogeneous group,
including Williams syndrome, familial elastin arteriopathy, sporadic cases, and others. This …

BACKGROUND: Supravalvular aortic stenosis is a rare stenotic lesion of the left ventricular
outflow tract (LVOT). We characterized the natural history of the disease and the effect of …

Objectives: Supravalvar aortic stenosis (SVAS) is a rare congenital anomaly. The “single-
patch technique,”“'two sinus augmentation with an inverted Y-patch”(both nonsymmetrical …

Objectives: To validate the conceptual framework of “criticality,” a new pediatric inpatient
severity measure based on physiology, therapy, and therapeutic intensity calibrated to care …