La obstrucción congénita al vaciamiento del ventrículo izquierdo, consistente en el
estrechamiento a uno o varios niveles de su porción de salida condicionando sobrecarga …

The objective of this paper is to describe the three-patch technique for repair of
supravalvular aortic stenosis (SVAS). Supravalvular aortic stenosis is a rare malformation as …

Les fibres élastiques, composées d'élastine (90%) et de microfibrilles riches en fibrilline
(10%), sont les principaux composants extracellulaires qui confèrent aux artères leur …

We report an extremely rare case of Williams–Beuren (WB) syndrome in a 10-year-old boy
with supravalvular aortic stenosis (SVAS) secondary to a large fibrocalcific eccentric shelf in …

Genetically mediated arteriopathies are a group of conditions characterized by abnormal
arterial microarchitecture with resultant deranged anatomic features and arterial function …

Many congenital heart defects with pulmonary valve pathology are repaired or palliated in
childhood. It is anticipated that these patients will need subsequent pulmonary valve …

Objective Supravalvar aortic stenosis (SVAS) is an uncommon congenital cardiac anomaly
characterized by varying degrees of left ventricular outflow tract obstruction distal to the …

Williams syndrome (WS) is a developmental disorder characterized by vascular
abnormalities such as thickening of the vascular media layer in medium-and large-sized …

Background Although repair of a supravalvular aortic stenosis (SVAS) can be performed
with low mortality rates, surgery for the complex form of SVAS continues to be associated …

Congenital left ventricular outflow tract obstruction accounts for 10% of all congenital heart
disease. The decision-making process and treatment management are challenging due to …