Inner ear malformations are predominantly attributed to developmental arrest during the
embryonic stage of membranous labyrinth development. Due to the inherent difficulty in …

About 20% of children with congenital hearing loss present malformations of the inner ear. In
the past few years much has been understood about the morphology and function of the …

Sensorineural hearing loss results from abnormalities that affect the hair cells of the
membranous labyrinth, inner ear malformations, and conditions affecting the auditory …

Objective Unilateral sensorineural hearing loss (USNHL) is a condition commonly
encountered in otolaryngology clinics. However, its molecular pathogenesis remains …

Detection of abnormalities within the inner ear is a challenging task even for experienced
clinicians. In this study, we propose an automated method for automatic abnormality …

Purpose This review aims to provides a comprehensive overview of the latest research
progress on IP-III inner ear malformation, focusing on its geneticbasis, imaging features …

The identification of congenital inner ear malformations is a challenging task even for
experienced clinicians. In this study, we present the first automated method for classifying …

Background. The genes involved in inner ear development and maintenance of the adult
organ have yet to be fully characterized. Previous genetic analysis has emphasized the …

Developmental anomalies of the hearing organ, the cochlea, are diagnosed in
approximately one-fourth of individuals with congenital deafness. Most patients with …

Wildervanck syndrome (also known as cervico-oculo-acoustic dysplasia) is a very rare
disease, characterized by the typical triad of cervical vertebral fusion or Klippel-Feil …