Adrenocortical carcinoma

E Baudin - Endocrinology and Metabolism Clinics, 2015 - endo.theclinics.com
Adrenocortical carcinoma (ACC) originates from the adrenal cortex and is typically defined
by positive immunostaining for steroidogenic factor 1 (SF1), melanA (Mart1) markers but …

Approach to the patient with adrenocortical carcinoma

A Lacroix - The Journal of Clinical Endocrinology & Metabolism, 2010 - academic.oup.com
Adrenocortical cancer (ACC) is a rare and often aggressive malignancy that requires
multidisciplinary expertise for optimal management. It can present with symptoms of rapidly …

Adrenocortical carcinoma: a clinician's update

M Fassnacht, R Libé, M Kroiss, B Allolio - Nature Reviews …, 2011 - nature.com
Adrenocortical carcinoma is a rare heterogeneous neoplasm with an incompletely
understood pathogenesis and a poor prognosis. Previous studies have identified …

Update in adrenocortical carcinoma

M Fassnacht, M Kroiss, B Allolio - The Journal of Clinical …, 2013 - academic.oup.com
Adrenocortical carcinoma (ACC) is an orphan malignancy that has attracted increasing
attention during the last decade. Here we provide an update on advances in the field since …

Adrenocortical carcinoma: clinical update

B Allolio, M Fassnacht - The Journal of Clinical Endocrinology & …, 2006 - academic.oup.com
Context: Adrenocortical carcinoma (ACC) is a rare and heterogeneous malignancy with
incompletely understood pathogenesis and poor prognosis. Patients present with hormone …

Management of endocrine disease: adrenocortical carcinoma: differentiating the good from the poor prognosis tumors

A Jouinot, J Bertherat - European Journal of Endocrinology, 2018 - academic.oup.com
Adrenocortical carcinoma (ACC) is a rare malignancy with a poor prognosis, the five-years
overall survival being below 40%. However, there is great variability of outcomes and we …

Adrenocortical carcinoma: past, present, and future

J Lafemina, MF Brennan - Journal of surgical oncology, 2012 - Wiley Online Library
Adrenocortical carcinoma (ACC) is a rare endocrine malignancy. Due to its rarity,
heterogeneity, and a lack of a comprehensive understanding of the pathogenesis, little …

Adrenocortical carcinoma: clinical outcomes and prognosis of 330 patients at a tertiary care center

M Ayala-Ramirez, S Jasim, L Feng… - European journal of …, 2013 - academic.oup.com
Objective Adrenocortical carcinoma (ACC) is a rare malignancy with a poor prognosis.
Herein, we describe the clinical features and outcomes for a large series of ACC patients …

Diagnostic and prognostic features in adrenocortical carcinoma: a single institution case series and review of the literature

KN Wanis, R Kanthan - World Journal of Surgical Oncology, 2015 - Springer
Background Adrenocortical carcinoma is a rare cancer, with an incidence in the literature of
0.5 to 2 cases per million population per year. Adult adrenocortical carcinoma has a poor …

Adrenocortical carcinoma: a comprehensive immunohistochemical study of 40 cases

A Weissferdt, A Phan, S Suster… - … & Molecular Morphology, 2014 - journals.lww.com
Adrenocortical carcinomas (ACC) are uncommon tumors of the adrenal cortex that are
known to follow an aggressive clinical course. The distinction of these tumors from other …