Background A brief bedside test has recently been introduced by Hoche et al.(Brain, 2018)
to screen for the Cerebellar Cognitive Affective Syndrome (CCAS) in patients with cerebellar …

Background The cerebellar cognitive affective syndrome scale (CCAS-S) was recently
developed to detect specific neuropsychological deficits in patients with cerebellar diseases …

Spinocerebellar ataxias (SCAs) are characterized by a heterogeneous set of clinical
manifestations. Our aims were to assess the neurological features of SCA3, and to describe …

Background Traditionally, cerebellar disorders including ataxias have been associated with
deficits in motor control and motor learning. Since the 1980's growing evidence has …

We thank Thieme et al.(2020a) for their letter, and we appreciated the opportunity to
participate in the translation of the Cerebellar Cognitive Affective Syndrome …

The cerebellar cognitive affective syndrome scale (CCAS-S) was designed to detect specific
cognitive dysfunctions in cerebellar patients but is scarcely validated in spinocerebellar …

Abstract The Cerebellar Cognitive Affective/Schmahmann Syndrome (CCAS) manifests as
impaired executive control, linguistic processing, visual spatial function, and affect …

Autosomal dominantly inherited ataxias are a clinically and genetically heterogeneous
group of neurodegenerative disorders. The gene involved in one subtype, spinocerebellar …

Highlights•Cognitive impairment in SCAs is well-established, but not universal in all
patients.•The CCAS Scale is the current standard for identifying cognitive impairments in …

RESULTS AND DISCUSSION The number of combined CTA/CTG repeats in the expanded
alleles of the hereditary cases were 97, 118, 119, 121, 125, 128, 128, 151, 151, 196, 199 …