OBJECTIVE. Schwannomas are typically benign tumors that occur sporadically, in
neurofibromatosis type 2 (NF2), or in an entity called “schwannomatosis.” Schwannomatosis …

The neurofibromatoses are a diverse group of genetic conditions that share a predisposition
to the development of tumors of the nerve sheath. Schwannomatosis is a recently …

Background Schwannomatosis is a recently recognized peripheral nerve polyneoplasm with
clinical characteristics and a genetic background that differ from those of neurofibromatosis …

Schwannomatosis is a recently delineated inherited condition that has clinical overlap with
neurofibromatosis type 2 (NF2). Diagnostic criteria have been developed to distinguish …

BACKGROUND: Schwannomatosis is a rare tumor syndrome characterized by the presence
of multiple schwannomas without the stigmata of neurofibromatosis (NF) Type 1 or 2. To …

Background: Schwannomatosis is a recently recognized disorder, defined as multiple
pathologically proven schwannomas without vestibular tumors diagnostic of …

Background: Schwannomatosis includes multiple cutaneous schwannomas, central nervous
system tumors and various neurologic deficits. Objective: To specify the clinical presentation …

Object The aim of this study was to provide disease-specific information about
schwannomatosis in its different forms and to present 2 particular cases of malignant …

Schwannomas are benign nerve sheath tumors that most commonly occur singularly in
otherwise normal individuals. Multiple schwannomas in a single patient are most often seen …

Background Data Schwannomatosis has become a newly recognized classification of
neurofibromatosis. Although the genetic loci are on chromosome 22, it lacks the classic …