Magnetic resonance imaging detects improvements of pulmonary and paranasal sinus abnormalities in response to elexacaftor/tezacaftor/ivacaftor therapy in adults …
L Wucherpfennig, SMF Triphan, S Wege… - Journal of Cystic …, 2022 - Elsevier
Abstract Background Therapy with Elexacaftor/Tezacaftor/Ivacaftor (ETI) was recently
approved for adult cystic fibrosis (CF) patients with at least one F508del mutation. However …
approved for adult cystic fibrosis (CF) patients with at least one F508del mutation. However …
Chest computed tomography improvement in patients with cystic fibrosis treated with elexacaftor-tezacaftor-ivacaftor: Early report
R Bec, M Reynaud-Gaubert, F Arnaud, R Naud… - European Journal of …, 2022 - Elsevier
Abstract Rationale and Objectives Cystic fibrosis transmembrane conductance regulator
(CFTR) modulators have revolutionised the treatment of cystic fibrosis (CF). Chest computed …
(CFTR) modulators have revolutionised the treatment of cystic fibrosis (CF). Chest computed …
Effects of elexacaftor/tezacaftor/ivacaftor therapy on lung clearance index and magnetic resonance imaging in patients with cystic fibrosis and one or two F508del …
SY Graeber, DM Renz, M Stahl… - American journal of …, 2022 - atsjournals.org
Rationale: We recently demonstrated that triple-combination CFTR (cystic fibrosis
transmembrane conductance regulator) modulator therapy with elexacaftor/tezacaftor …
transmembrane conductance regulator) modulator therapy with elexacaftor/tezacaftor …
Clinical effectiveness of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis: a clinical trial
DP Nichols, AC Paynter, SL Heltshe… - American journal of …, 2022 - atsjournals.org
Rationale: The cystic fibrosis (CF) modulator drug, elexacaftor/tezacaftor/ivacaftor (ETI),
proved highly effective in controlled clinical trials for individuals with at least one F508del …
proved highly effective in controlled clinical trials for individuals with at least one F508del …
[HTML][HTML] Elexacaftor-Tezacaftor-Ivacaftor improves sinonasal outcomes in cystic fibrosis
AL Stapleton, AJ Kimple, JL Goralski, SM Nouraie… - Journal of Cystic …, 2022 - Elsevier
Background Many individuals with cystic fibrosis (CF) have chronic rhinosinusitis resulting in
nasal obstruction, sinus infections, and repeated surgeries. Elexacaftor-tezacaftor-ivacaftor …
nasal obstruction, sinus infections, and repeated surgeries. Elexacaftor-tezacaftor-ivacaftor …
Improvement in lung clearance index and chest computed tomography scores with elexacaftor/tezacaftor/ivacaftor treatment in people with cystic fibrosis aged 12 …
Rationale: Clinical trials have shown that use of elexacaftor/tezacaftor/ivacaftor (ETI) is
associated with improvements in sweat chloride, pulmonary function, nutrition, and quality of …
associated with improvements in sweat chloride, pulmonary function, nutrition, and quality of …
[HTML][HTML] Computed tomography correlates with improvement with ivacaftor in cystic fibrosis patients with G551D mutation
SI Sheikh, FR Long, KS McCoy, T Johnson… - Journal of Cystic …, 2015 - Elsevier
Background Ivacaftor corrects the cystic fibrosis transmembrane conductance regulator
(CFTR) gating defect associated with G551D mutation and is quickly becoming an important …
(CFTR) gating defect associated with G551D mutation and is quickly becoming an important …
[HTML][HTML] Effect of highly effective modulator treatment on sinonasal symptoms in cystic fibrosis
E DiMango, J Overdevest, C Keating, SF Francis… - Journal of Cystic …, 2021 - Elsevier
Background Elexacaftor-tezacaftor-ivacaftor is a highly effective modulator for cystic fibrosis
(CF) patients homozygous or heterozygous for F508del. Effects of the drug on sinonasal …
(CF) patients homozygous or heterozygous for F508del. Effects of the drug on sinonasal …
The French compassionate programme of elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis with advanced lung disease and no F508del CFTR variant
PR Burgel, I Sermet-Gaudelus, I Durieu… - European …, 2023 - Eur Respiratory Soc
Background The European Medicines Agency has approved the cystic fibrosis
transmembrane conductance regulator (CFTR) modulator combination …
transmembrane conductance regulator (CFTR) modulator combination …
Effects of elexacaftor/tezacaftor/ivacaftor therapy in children with cystic fibrosis–a comprehensive assessment using lung clearance index, spirometry, and functional …
C Streibel, CC Willers, O Pusterla, G Bauman… - Journal of cystic …, 2023 - Elsevier
Background With improvement in supportive therapies and the introduction of cystic fibrosis
transmembrane conductance regulator (CFTR)-modulator treatment in patients with cystic …
transmembrane conductance regulator (CFTR)-modulator treatment in patients with cystic …
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