Pleuroparenchymal fibroelastosis (PPFE) is an unusual pulmonary disease with unique
clinical, radiological, and pathological characteristics. Designated a rare idiopathic …

Pleuroparenchymal fibroelastosis (PPFE) is a rare condition characterised by predominantly
upper lobe pleural and subjacent parenchymal fibrosis, the latter being intra-alveolar with …

Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently described clinical-
pathologic entity characterized by pleural and subpleural parenchymal fibrosis, mainly in the …

Pleuroparenchymal fibroelastosis (PPFE) is a rare pulmonary fibrosis that is clinically
characterized by upperlobe predominant fibrosis. PPFE is a slowly progressive disorder and …

Idiopathic pleuroparenchymal fibroelastosis is a rare recently described entity likely to be
under-and misdiagnosed, as awareness of this entity is not yet widespread. We report two …

Pleuroparenchymal fibroelastosis (PPFE) is a distinct pattern of pulmonary fibrosis which
often runs a rapidly progressive course with a poor prognosis, and it is likely to be …

Purpose of the review Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare fibrosing
lung disease, affecting the visceral pleura and the subpleural parenchyma with an upper …

Between 1996 and 2001, we identified five cases of a unique idiopathic pleuroparenchymal
lung disease characterized by a clinical presentation suggestive of a chronic idiopathic …

Background Although the accurate diagnosis of pleuroparenchymal fibroelastosis (PPFE)
requires pathologic evaluation, this diagnosis is often suggested when the radiologic …

Background Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a recently reported
group of disorders characterized by fibrotic thickening of the pleural and subpleural …