Although these conditions are rare, a proportion of patients with interstitial lung diseases
(ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated …

Acute exacerbation of interstitial lung disease (ILD) is associated with a poor prognosis and
high mortality. Numerous studies have documented acute exacerbation in idiopathic …

A proportion of patients with interstitial lung diseases (ILDs) are at risk of developing a
progressive-fibrosing phenotype, which is associated with a deterioration in lung function …

The availability of epidemiological data relating to interstitial lung diseases (ILDs) has
increased over recent years, but information on the prevalence and incidence of ILDs of …

Despite conventional treatment, a proportion of interstitial lung disease (ILD) patients
develop a progressive phenotype known as “fibrosing ILD with a progressive phenotype”(PF …

Objective: Some patients with interstitial lung diseases (ILDs) other than idiopathic
pulmonary fibrosis (IPF) develop a progressive fibrosing phenotype. We investigated the …

Background: The prevalence and natural history of progressive fibrosing interstitial lung
diseases (PF-ILDs), and their response to commonly used treatments in real life are largely …

Background Progressive fibrosing interstitial lung disease (PF-ILD) is characterised by
progressive physiological, symptomatic and/or radiographic worsening. The real-world …

Establishing the etiology of fibrosing interstitial lung disease (FILD) remains a clinical
challenge. This is because many disorders resulting in lung fibrosis may be similar in their …

Fibrotic interstitial lung diseases (ILDs) are often challenging to diagnose and classify, but
an accurate diagnosis has significant implications for both treatment and prognosis. A …